高禹舜 汪良骏 张大为 张汝刚 张德超 杨林 100021 北京，中国医学科学院中国协和医科大学肿瘤研究所肿瘤医院胸外科 中华肿瘤杂志 1999 0 21 6


    关键词：食管肿瘤/外科学；平滑肌肉瘤/外科学；预后 期刊 zhzlzz 0 临床应用 fur -->


    

【摘要】 目的 探讨食管平滑肌肉瘤的临床生物学特征、诊断方法、手术方式及其预后。方法 总结分析11例食管平滑肌肉瘤的诊断及手术治疗经验。结果 本组11例手术切除率为100%，5年生存率为54.5%(6/11)。诊断主要依靠食管造影、拉网及纤维食管镜(FOE)。临床分为息肉型和侵袭型，本组息肉型4例，侵袭型7例，5年生存率分别为3例/4例和3例/7例。远期肿瘤死于局部复发2例，血行转移2例。结论 食管平滑肌肉瘤的预后优于食管癌，息肉型预后优于浸润型。远期肿瘤死因为局部复发及血行转移。本病手术切除率高，宜采取手术治疗。

Surgical treatmentof esophageal leiomyosarcoma: a review of the literature and report of 11 cases

GAO Yushun, WANG Liangjun, ZHANG Dawei, et al. CancerHospital(institate), Chinese Academy of Medical Sciences, Peking Union Medical College.Beijing 100021

【Abstract】 Objective To discuss theclinical biocharacteristics, diagnosis, operation and prognosis of esophagealleiomyosarcoma (ELS). Methods Clinical materials and follow-up resultsof 11 surgically treated ELS patients were analyzed. Results All 11cases received radical resection of tumor. The 5-year survival rate was 54.5% (6/11).Grossly, two types of ELS were observed: the polyp form (4 cases) and invasive form (7cases). The 5-year survival rate was 75.0% and 42.9%, respectively. Two patients died oflocal recurrence, another 2 cases died of distant metastasis. Conclusion Inpatients with ELS surgically treated, prognosis of polyp form ELS is better than that ofinvasive form ELS. Local recurrence and distant metastasis are the major cause of death.

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