【摘要】 目的 提高对肺淋巴管平滑肌瘤病(pulmonary lymphangiomyomalosis,PLAM)的影像学认识，并引起对该病的重视。方法 经手术与病理证实为PLAM的4例女性患者均做了胸部X线及HRCT检查。结果 胸片示早期双肺弥漫网状阴影，晚期呈蜂窝样改变。HRCT表现为双肺广泛分布的薄壁小囊样病变。结论 PLAM是一种原因不明的慢性肺间质病变。育龄期妇女如反复出现自发性气胸、痰血、活动后呼吸困难，临床上应考虑PLAM可能。

    【关键词】 肺淋巴管平滑肌瘤病变；胸部；X线；计算机

    X-ray and CT imaging diagnosis of the pulmonary lymphangiomyomatosic:a report of 4 cases

    ZHANG Ai-hui,ZHANG Jin-ting,CHI Hong-wei.

    The People′s Hospital of Yuzhou,Yuzhou 461670,China

    【Abstract】 Objective To improve the imaging recognition of the pulmonary lympha

    ngiomgomatosis (PLAM) and to pay more atcention to it.Methods 4 cases of PLAM confirmed by operation and pathology were reported,chest X-ray and HRCT was perfomed in all 4 cases . Results ......