【摘要】 目的 探讨单纯前庭水管扩大综合征(LVAS)的发病机制、临床表现、诊断治疗及预防。方法 回顾性分析我院LVAS 8例(14耳)患者的临床特点、听力学及CT检查，并复习文献。结果 8例经CT检查结合临床表现均确诊为LVAS。结论 LVAS为前庭水管先天发育宽大畸形，出生后或少儿时出现感音神经性耳聋，高分辨螺旋CT可以确诊。目前保守治疗缺乏特效性，可以选择性行电子耳蜗植入术。

    【关键词】 前庭水管；扩大；畸形；井喷

    Enlarged vestibular aqueduct syndrome:a clinical analysis of 8 cases

    ZHANG En-dong,LIU Xin-yi,SUN Cai-bo,et al.

    The Second Hospital of Weihai,Weihai 264200,China

    【Abstract】 Objective To evaluate the pathogenesis,clinical feature,diagnosis,prevention and treatment of the enlarged vestibular aqueduct syndrome.Methods The clinical characters,audiology and CT test of 8 patients with the enlarged vestibular aqueduct syndrome were studied retrospectively.In addition the literatures were reviewed.Results 8 cases were all diagnosed as the enlarged vestibular aqueduct syndrome.Conclusion LVAS is the congenital enlarged abnormalities of vestibular aqueduct,with the sensorineural hearing loss after birth or in childhood,that are diagnosed by the high-resolution compution tomography.Now conservative ......