摘 要 目的：提高对肺结节病的认识和诊断符合率。方法：对1990～2007年经病理确诊为结节病8例患者的临床误诊资料作回顾性分析。结果：肺结节病临床表现不典型，胸部 X线及CT常表现为肺门增大，以双侧肺门肿大为主，易误诊为肺结核或肿瘤。经纤维支气管镜活检或皮肤粘膜、淋巴结活检可确诊。结论：肺结节病多见于青中年人，女性发病率高，临床症状不典型，在诊断上要结合临床表现、胸片以及纤维支气管镜检、皮肤粘膜、淋巴结活检进行病理检查。

    关键词 肺结节病；临床表现；诊断

    Abstract Objective：To improve the recognition and the diagnostic accuracy of pulmonary sarcoidosis. Methods： The clinical misdiagnosed data of 8 cases of sarcoidosis confirmed by pathology during the year of 1990 -2007 were retrospectively analyzed. Results: The clinical manifestations of pulmonary sarcoidosis were not typical. Its chest X-ray and CT scans showed the enlargement of lung hilum and frequently presented with bilateral hilar lymphadenopathy, liable to be misdiagnosed as tuberculosis or tumor. Diagnosis were made through transbronchial lung biopsy and biopsy of skin, mucosa and lymph node. Conclusions： Intrathoracic sarcoidosis has atypical clinical symptoms, commonly affects young and middle-aged adults and slightly higher disease rate for women. To improve diagnosis accuracy, we should combine clinical symptom of pulmonary sarcoidosis with chest X-ray and pathology biopsy of bronchofiberoscopy, skin, mucosa and lymph node. ......