Mechanism of Residence of Cytochrome b(5), a Tail-anchored Protein, in
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《细胞学杂志》
a Consiglio Nazionale Ricerche Cellular and Molecular Pharmacology Center, Department of Pharmacology, University of Milan, Italy 20129
b Biological and Technological Research Department, Scientific Institute San Raffaele, Milan, Italy 20132
c Consiglio Nazionale Ricerche Institute of Biocatalysis and Molecular Recognition, Milan, Italy 20133
d Faculty of Pharmacy, University of Catanzaro "Magna Graecia", Roccelletta di Borgia (Catanzaro), Italy 88021
Correspondence to: Nica Borgese, Consiglio Nazionale Ricerche Cellular and Molecular Pharmacology Center, via Vanvitelli 32, 20129 Milan, Italy. Tel:39-02-7014-6250 Fax:39-02-7490-574 E-mail:nica@farma.csfic.mi.cnr.it.
Abstract
Endoplasmic reticulum (ER) proteins maintain their residency by static retention, dynamic retrieval, or a combination of the two. Tail-anchored proteins that contain a cytosolic domain associated with the lipid bilayer via a hydrophobic stretch close to the COOH terminus are sorted within the secretory pathway by largely unknown mechanisms. Here, we have investigated the mode of insertion in the bilayer and the intracellular trafficking of cytochrome b(5) (b), taken as a model for ER-resident tail-anchored proteins. We first demonstrated that b(5) can acquire a transmembrane topology posttranslationally, and then used two tagged versions of b(5), N-glyc and O-glyc b(5), containing potential N- and O-glycosylation sites, respectively, at the COOH-terminal lumenal extremity, to discriminate between retention and retrieval mechanisms. Whereas the N-linked oligosaccharide provided no evidence for retrieval from a downstream compartment, a more stringent assay based on carbohydrate acquisition by O-glyc b(5) showed that b(5) gains access to enzymes catalyzing the first steps of O-glycosylation. These results suggest that b(5) slowly recycles between the ER and the cis-Golgi complex and that dynamic retrieval as well as retention are involved in sorting of tail-anchored proteins.
Key Words: cell compartmentation, endoplasmic reticulum, glycosylation, Golgi apparatus, membrane proteins
Introduction
Notwithstanding the intense membrane traffic taking place within eukaryotic cells, subcellular compartments maintain their molecular identity with remarkable accuracy. Within the secretory pathway, proteins that reside in a given compartment must avoid being relocated to neighboring compartments in the face of ongoing transport. Two different mechanisms, static retention and dynamic retrieval, can, in principle, ensure that each compartment keeps its cohort of resident proteins. Retained proteins are thought to be simply excluded from transport out of their compartment of residence, whereas retrieved proteins do escape to a downstream organelle from which they are recycled by retrograde transport (Pelham and Munro 1993 ).
Consistent with its diverse functions, the membrane of the ER has a complex molecular composition, and many studies have been devoted to the mechanisms through which it keeps its numerous resident polypeptides from following transported proteins down the secretory pathway. These studies have shown that both retrieval via coat protein I–coated vesicles and retention are operative in determining residence of ER membrane proteins (for review see Teasdale and Jackson 1996 ). Of the two mechanisms, the former is better understood, and retrieval signals have been identified in the cytosolic tails of type I and type II ER resident membrane proteins (Cosson and Letourneur 1994 ; Teasdale and Jackson 1996 ; Cosson et al. 1998 ). In addition, a number of membrane proteins are retrieved by interaction of their transmembrane domains (TMDs)1 with a recently identified receptor, rer1p (Sato et al. 1996 , Sato et al. 1997 ). Less information is available on static retention. Although it could be argued that retention is effected simply by the absence of positive signals required for efficient recruitment of cargo protein into transport vesicles (Springer et al. 1999 ), it is likely that specific retention signals or features are also necessary to prevent access of retained proteins into budding vesicles (Sonnichsen et al. 1994 ).
Although there is evidence that both retrieval and retention operate at the ER–Golgi complex boundary, an important question that is still largely unresolved are the relative roles played by these two mechanisms in determining the residency of ER membrane proteins. Posttranslational modifications are generally used to follow intracellular trafficking between the ER and the Golgi. However, many ER membrane proteins do not have consensus sites for such modifications and are thus difficult to study. For instance, membrane proteins with the so-called tail-anchored (TA) topology, consisting of an NH2-terminal active cytosolic domain and a hydrophobic membrane-anchoring region close to the COOH terminus, essentially lack a lumenal domain (for reviews see Borgese et al. 1993 ; Kutay et al. 1993 ). Many ER enzymes whose catalytic activity is at the cytosolic side of the membrane have a TA topology, e.g., cytochrome b(5) (b), heme oxygenase, aldehyde dehydrogenase, and ubiquitin conjugating enzyme 6, and unraveling their sorting mechanisms would make an important contribution to our understanding of the genesis and maintenance of the molecular identity of the ER. In our laboratory we have been using b(5) as a model to study the targeting and sorting of ER-resident TA proteins. b(5) is an ~15,000-Mr protein with an NH2-terminal, globular cytosolic heme-binding domain, a short connecting region, and a hydrophobic anchoring domain followed by seven polar residues at the extreme COOH terminus (for review see Borgese et al. 1993 ). Since ER-resident TA enzymes generally have short hydrophobic anchoring domains (14–18 residues), we investigated a possible role of the length of the hydrophobic domain in sorting and demonstrated that a short anchoring domain is required to keep b(5) from escaping from the ER and from travelling down the secretory pathway to the cell surface (Pedrazzini et al. 1996 ). A similar observation was subsequently made on other ER-resident TA proteins (Rayner and Pelham 1997 ; Yang et al. 1997 ), establishing the generality of tail length–dependent sorting. However, an open question remained as to whether the short hydrophobic domain effects ER residence of TA proteins by a static retention or by a dynamic retrieval mechanism. In this study, we have investigated this question. Using tagged versions of b(5) with N- or O-glycosylation sites attached at the COOH terminus, we show that b(5) gains access to enzymes catalyzing the first steps of O-glycosylation, suggesting that it slowly recycles between the ER and the cis-Golgi.
Materials and Methods
Plasmid Constructions
A cDNA coding for the rabbit ER form of b(5) (Giordano and Steggles 1992 ) and subcloned into pGEM 4 and into the mammalian expression vector pCB6 (Brewer and Roth 1991 ), has been described in previous work (Pedrazzini et al. 1996 ). We refer to the protein expressed from this plasmid as wild-type (wt) b(5).
To facilitate addition of sequence tags at the COOH terminus of b(5), we introduced a unique Age1 site at the border between the hydrophobic domain and the extreme COOH-terminal polar region, which did not alter the encoded amino acid sequence, and Xba1 and Hind3 sites immediately after the stop codon. The three restriction sites were introduced by substituting a 3' terminal Aat2-Hind3 620-bp fragment of wt b(5) in pGEM4 (the Aat2 site at position 335 and the Hind3 site in the polylinker) with a 214-bp, PCR-generated fragment. The resulting plasmid (pGbAX) was used to construct the N-glyc b(5) and O-glyc b(5) mutants, which contained, close to their COOH termini, potential N- and O-glycosylation sites, respectively. The 25-bp Age1-Xba1 fragment of pGb(5)AX was replaced with an 89-bp duplex or 86-bp duplex obtained by annealing two complementary synthetic oligonucleotides coding for the sequences illustrated in Fig 2 A. The constructs were checked by sequencing and then subcloned into the Kpn1-Hind3 sites of pCB6 with a modified polylinker (De Silvestris et al. 1995 ).
Figure 1. The COOH-terminal polar peptide of b(5) is inaccessible to Ab if the ER membrane is not permeabilized. MDCK cells overexpressing wt b(5) were permeabilized with SLO (5 U/ml; see Materials and Methods), then fixed and processed for immunofluorescence in the presence (C, D, G, and H) or absence (A, B, E, and F) of Triton X-100. Cells were doubly labeled with the following pairs of Abs: polyclonal Ab raised against the 10 COOH-terminal amino acids of b(5) (A and C) and antitubulin mAb (B and D); polyclonal Ab against the catalytic domain of b(5) (E and G) and anti-PDI mAb (F and H). Polyclonal and monoclonal Abs were viewed with TRITC- and FITC-conjugated secondary Abs, respectively. The panels on the left and right side of the figure represent the same fields viewed under the rhodamine or fluorescein filters. Fields of cells treated or not treated with Triton X-100 were photographed and printed with the same exposures. Bar, 10 μm.
Figure 2. In vitro translated N-glyc b(5) becomes glycosylated in the presence of dog pancreas microsomes added either during or after translation. (A) COOH-terminal sequences of wt b(5) and of the N-glyc and O-glyc constructs. In all constructs, the hatched rectangle represents the COOH-terminal part of the membrane-anchoring domain. The underlined sequence in N-glyc b(5) corresponds to the first 19 amino acids of bovine opsin, and is connected to the COOH terminus of b(5) through a Ser and an Arg residue (italics). An N-glycosylation consensus sequence is boxed. The underlined sequence of O-glyc b(5), connected to the COOH terminus of b(5) via the SR sequence (italics), corresponds to residues 36–48 and residue 50 of mature human glycophorin A. The residues in boldface (Y between V48 and T50 and the three COOH-terminal prolines) were included to create an optimal consensus for O-glycosylation (Yoshida et al. 1997 ). The boxed residues are those that are glycosylated in native glycophorin A (Tomita and Marchesi 1975 ). (B) N-glyc b(5) (upper panel) or bean phaseolin (lower panel) synthetic RNAs were translated for 1 h in the rabbit reticulocyte system in the presence (lanes 1 and 2; Mbs co) or absence (lanes 3–6) of dog pancreas microsomes. One sample, which was first incubated in the absence of microsomes, was then treated with CHX, subjected to ultracentrifugation to remove ribosomes (see Materials and Methods), and further incubated for 1 h with microsomes (lanes 5 and 6; Mbs post). At the end of the incubations, samples were divided into two, denatured with SDS, and then incubated overnight in the presence (lanes 2, 4, and 6) or absence (lanes 1, 3, and 5) of Endo H (see Materials and Methods). The arrow in the upper panel indicates the Endo H–sensitive polypeptide (glycosylated N-glyc b) generated when microsomes were present during or after translation. The single and double asterisks in the lower panel indicate the mono- and diglycosylated forms of phaseolin, respectively (Ceriotti et al. 1991 ), which were generated only when membranes were present during the translation. Numbers on the left indicate the position and size (in kD) of Mr markers.
Cell Culture and Transfection
Most of the experiments in this study were conducted on transiently transfected CV1 cells that were cultured and transfected with the Ca2+PO4 method as described previously (De Silvestris et al. 1995 ). The efficiency of transfection was usually monitored by cotransfecting with green fluorescent protein (Clontech). For the fractionation experiment (see Fig 10), transfection was carried out with lipofectamine (GIBCO BRL) with 0.03 μg of b(5) cDNA/cm2 of culture dish surface. Cells were used for immunofluorescence or biochemical experiments within 24 h after transfection. In one experiment (see Fig 1), an MDCK line stably expressing wt b(5) was used. MDCK cells were cultured and transfected as described previously (Borgese et al. 1996 ). Several b(5)-expressing clones were obtained; however, the expression was completely lost after only a few passages in culture, so that further experiments with these clones could not be carried out.
Figure 3. Comparison of the distribution of overexpressed wt b(5) with that of endogenous ERGIC 53 in transfected CV1 cells incubated at 37 or 15°C. Transfected cells were incubated in DME, Hepes modification (Sigma Chemical Co.) in thermostated water baths for 5 h at 37°C (A–C) or 15°C (D–F), fixed and permeabilized, and doubly stained with anti-b(5) mAbs followed by TRITC-conjugated anti–mouse IgG (A and D), and polyclonal anti–ERGIC 53 followed by FITC-conjugated anti–rabbit IgG (B and E). A single confocal section is shown for each incubation condition. Images of the same field were acquired separately with Texas red (A and D) and fluorescein (B and E) filters. C and F show the merged images of the two acquisitions. Bar, 10 μm.
Figure 4. Velocity gradient analysis of b(5) solubilized from rat liver microsomes or transfected CV1 cells. Rat liver microsomes (A) or CV1 cells transfected with wt b(5) cDNA were lysed and loaded onto a 5–20% sucrose gradient containing 0.2% Triton X-100 and low salt, as described in Materials and Methods. Fractions were analyzed by Western blotting. Ribophorin (R) forms aggregates which distribute throughout the gradient and sediment into the pellet, whereas b(5) is found only in the top fractions, cosedimenting with cytochrome c. The vertical large and small arrowheads in both panels indicate the positions reached by cytochrome c (Mr ~12,300) and catalase (Mr ~232,000), respectively. Numbers on the left of the panels indicate the position and size (in kD) of Mr markers used in the Western blot analysis.
Figure 5. N-glyc and O-glyc b(5) have a reticular distribution in transfected cells and their catalytic domain is accessible to Abs restricted to the cytosol. CV1 cells transfected with N-glyc b(5) (A and B) or O-glyc b(5) (C and D) cDNA were permeabilized with SLO (30 μg/ml), and then fixed and doubly stained with mAbs against the catalytic domain of b(5) followed by TRITC-conjugated anti–mouse IgG (A and C), and with polyclonal Abs against the cytosolic tail of ERGIC 53 followed by FITC-conjugated anti–rabbit IgG (B and D). The figure shows single confocal sections of one field for each construct. The panels on the left and right side of the figure represent the same fields acquired with the Texas red or fluorescein filters. Asterisks indicate the nuclei of transfected cells. Note the clear staining of the nuclear envelope by anti-b(5) Abs both in N-glyc and O-glyc b(5)–transfected cells, indicative of ER localization. Bar, 10 μm.
Figure 6. The N-linked oligosaccharide of N-glyc b(5) retains Endo H sensitivity and Endo D resistance. (A) CV1 cells transfected with N-glyc b(5) cDNA were labeled for 2 h with Met/Cys, then chased for a further 6 h. One set of cells was exposed to BFA (10 μg/ml) 30 min before starting the labeling, and was kept with the drug for the entire pulse and chase period (lanes 5 and 6). At the end of the pulse (lanes 1 and 2) or after the chase (lanes 2–6), cells were harvested, lysed, and subjected to immunoprecipitation with antiopsin mAbs. Aliquots containing the same amounts of incorporated radioactive amino acid were used for each immunoprecipitation. One half of each immunoprecipitate was treated with Endo H (lanes 2, 4, and 6), whereas the other half was left untreated (lanes 1, 3, and 5). (B) CHO 15B cells, transfected with N-glyc b(5) cDNA, were labeled for 2 h and chased for 6 h with Met/Cys. One set of cells (lanes 3 and 4) was exposed to BFA as in A. At the end of the chase period, cells were harvested, lysed, and subjected to immunoprecipitation as in A. One half of the immunoprecipitates was treated with Endo D (lanes 2 and 4), whereas the other half was left untreated (lanes 1 and 3). The figure shows the result of the SDS-PAGE fluorography analysis of the Endo H– or Endo D–treated and untreated immunoprecipitates. The position of the 21-kD molecular mass marker is shown at the left of each panel. The vertical arrow in lane 2 of B indicates the position of the unglycosylated N-glyc b(5).
Figure 7. O-glyc b(5) becomes glycosylated in vivo. (A) Comparison of SDS-PAGE mobility of in vivo and in vitro synthesized O-glyc b(5). CV1 cells transfected with O-glyc b(5) cDNA were labeled for 2 h with Met/Cys, harvested, and subjected to immunoprecipitation with anti-b(5) Abs (lane 1). Alternatively, synthetic RNA coding for O-glyc b(5) was translated in vitro either in the absence (lane 2) or in the presence (lane 3) of dog pancreas microsomes. SDS-PAGE followed by fluorography fails to reveal a difference between the apparent Mr of the protein synthesized in vivo and that of the primary translation product produced in vitro. (B) Metabolic labeling of O-glyc b(5) with 3H-labeled sugars. CV1 cells, transfected with wt b(5) (lanes 1 and 2) or with O-glyc b(5) (lanes 3–6) cDNA, were incubated for 7 h with GlcNH2 (lanes 1–4) or Gal (lanes 5 and 6). For each labeling condition, one set of cells (lanes 2, 4, and 6) received 10 μg/ml of BFA 30 min before exposure to the labeled sugar, and the drug was maintained in the medium during the entire subsequent incubation. At the end of the incubation, cells were harvested, lysed, and aliquots containing the same amounts of incorporated radioactive sugar were subjected to immunoprecipitation with anti-b(5) Abs. Immunoprecipitates were analyzed by SDS-PAGE fluorography (upper panel). One fourth of the amounts used for immunoprecipitation were analyzed by Western blotting with anti-b(5) Abs (lower panel). The line on the left side of all panels indicates the position of the 21-kD molecular mass marker.
Figure 8. Time course of posttranslational addition of 3H-labeled sugar to O-glyc b(5). (A) Metabolic labeling with GlcNH2. Cells transfected with O-glyc b(5) were incubated for 3 h with GlcNH2 to allow for equilibration between UDP-GlcNAc and UDP-GalNAc. Cells from one dish were harvested at this point (lane 1), whereas the others were incubated for a further 1 (lanes 2 and 3) or 4 (lanes 4 and 5) h in the presence or absence of 15 μg/ml CHX as indicated. For each time point, cell lysates were prepared, and equal amounts of protein were used for immunoprecipitation with anti-b(5) Abs (upper panel). A proportional amount of each lysate (one fifth of the amount used for immunoprecipitation) was analyzed by Western blotting (lower panel). (B) Block of O-glyc b(5) synthesis by CHX. Cells transfected with O-glyc b(5) were incubated in parallel with those in A, but without added GlcNH2. After 3 h, Met/Cys was added and incubation was continued in the presence or absence of 15 μg/ml CHX, as indicated. At the indicated times, cell lysates were prepared and equal amounts of protein were used for immunoprecipitation, as in A. (C) Graphical representation of the results of A compared with the incorporation of 3H-labeled sugar into total protein. The graph on the right shows the ratios of band intensities of fluorographs (metabolically labeled O-glyc b) to those of the Western blots (total O-glyc b). Shown are the means from three sets of dishes ± SEM. The value for the ratio at 3 h (time of addition of CHX) has been normalized to 1. The graph on the left represents total TCA-precipitable 3H-labeled sugar normalized to total protein content. Squares, no CHX; triangles, CHX.
Figure 9. OKA inhibits sugar acquisition by O-glyc b(5). (A) CV1 cells transfected with O-glyc b(5) were incubated with GlcNH2 for 3 h to allow for equilibration between UDP-GlcNAc and UDP-GalNAc. At this time, one set of cells was harvested (lane 1), whereas the others were incubated for a further hour in the presence (lanes 4 and 5) or absence (lanes 2 and 3) of 1 μM OKA with or without 10 μg/ml BFA, as indicated. After clearing of lysates, equal amounts of protein were subjected to immunoprecipitation with anti-b(5) Abs (upper panel). A proportional amount of each lysate (one fifth of the amount used for immunoprecipitation) was analyzed by Western blotting (lower panel). (B) Graphical representation of the results of two experiments like the one in A. Two separate sets of dishes were labeled as described for A. The ratio of the intensities of the O-glyc b(5) bands detected by fluorography to that of the bands in corresponding samples detected by Western blotting is plotted. Shown are the means values ± half-range. (C) Immunofluorescence analysis of cells treated or not treated with 1 μM OKA. After 1 h with (C, panels d–f) or without (C, panels a–c) OKA, cells were fixed. Separate coverslips were analyzed for b(5) (C, panels a and d), ERGIC 53 (C, panels b and e), and giantin (C, panels c and f). Note the redistribution of ERGIC 53 induced by OKA, whereas O-glyc b(5) and giantin appear unaffected by the drug. Bar, 20 μm.
Figure 10. Intracellular distribution of O-glyc b(5). (A) O-glyc b(5) remains in the ER after prolonged incubation with CHX. CV1 cells transfected with O-glyc b(5) were incubated under the same conditions as in the experiments of Fig 8 and Fig 9, but without the labeled precursor and in the presence of 20 μg/ml of CHX for 4 (A, panels a–c) or 8 (A, panels d–f) h. Fixed cells were doubly labeled with anti-b(5) and anti–ribophorin I Abs (A, panels a–c), or with anti-b(5) and antigiantin Abs (A, panels d–f). A single confocal section is shown for the 4- and 8-h incubation. Images of the same field were acquired separately with the Texas red (A, panels a and d) and the fluorescein (A, panels b and e) filters. The corresponding merged images are shown in A, panels c and f (O-glyc b in red, marker protein in green). Note the absence of colocalization of O-glyc b(5) with giantin and its similar distribution to ribophorin I. The arrowheads in A, panels a–c indicate structures in which O-glyc b(5) accumulates at long times after transfection, and which are also positive for ribophorin I. Bar: (panels a–c) 10 μm; (panels d–f) 20 μm. (B) Optiprep density gradient analysis of CV1 cells transfected with O-glyc b(5) and metabolically labeled with GlcNH2. Cells were metabolically labeled with GlcNH2 for 6 h, then returned to DME for 4 h, before collection, homogenization, and preparation of a PNS, which was loaded under an 8–22% Optiprep gradient (see Materials and Methods). After centrifugation, fractions were collected and analyzed for O-glyc b(5) by Western blotting (B, panel a), NADPH-cyt c reductase enzyme activity (B, panel b), 3H-labeled O-glyc b(5) by immunoprecipitation followed by SDS-PAGE fluorography (B, panel c), and GS28 by Western blotting (B, panel d). The thick line positioned at the right of each graph covers the fractions containing the load zone of the gradient.
For the experiment shown in Fig 6 B we used CHO-15B cells grown in a 5% CO2 incubator in MEM with Earle's salts -modification, supplemented with 7.5% FCS, 2 mM glutamine, and antibiotics. These cells were transfected with the lipofectin (GIBCO BRL), using 0.2 μg of plasmid/cm2 of culture dish surface.
Antibodies
The following antibodies (Abs) were produced in our laboratory: (a) affinity-purified polyclonal Abs against b(5) raised in rabbits in our laboratory (Borgese and Meldolesi 1976 ; De Silvestris et al. 1995 ); (b) an affinity-purified polyclonal Ab directed against the 10 COOH-terminal residues of b(5). 2.4 mg of the peptide (LMYRLYMADD) was conjugated to 3 mg of chicken ovalbumin with succinimidyl 4--cyclohexane-1-carboxylate (Pierce) and used to immunize a rabbit. In addition, the following Abs were generously donated by the indicated investigators: a monoclonal anti-b(5) mAb from Dr. S. Park (Industrial Health Research Institute, Inchon, Korea) (Park et al. 1992 ); an antipeptide polyclonal antiserum against the 10 COOH-terminal amino acids of ERGIC 53 (QQEAAAKKFF) from Dr. Stefano Bonatti (University of Naples, Naples, Italy); polyclonal Abs against ribophorin I from Dr. Giovanni Migliaccio (Istituto di Ricerche di Biologia Molecolare, Pomezia, Italy) (Nicchitta et al. 1991 ) and Dr. Gert Kreibich (New York University School of Medicine, New York, NY) (Yu et al. 1990 ); an anti–? tubulin mAb (DM1) from Dr. Mark Kirschner (Harvard Medical School, Boston, MA); a mAb against the NH2-terminal peptide of bovine opsin (R2-15) from Dr. Paul Hargrave (University of Florida, Gainesville, FL) (Adamus et al. 1991 ); an antigiantin polyclonal serum from Dr. M. Renz (Institute of Immunology and Molecular Genetics, Karlsruhe, Germany) (Seelig et al. 1994 ). Anti–protein disulfide isomerase (PDI) and anti-GS28 mAbs were from StressGen Biotechnologies.
Immunofluorescence
Paraformaldehyde-fixed cells were permeabilized with Triton X-100 and processed for immunofluorescence as described previously (De Silvestris et al. 1995 ). In some experiments, permeabilization of the plasma membrane was carried out with streptolysin O (SLO), obtained from Dr. S. Bhakdi (Johannes-Gutenberg Universit?t, Mainz, Germany) (Bhakdi et al. 1993 ). Cells grown on coverslips were incubated with a buffer containing 115 mM K+acetate, 25 mM Hepes-KOH, pH 7.0, 2.5 mM MgCl2, 0.2 mM CaCl2, 1 mM EGTA, 12 mM glucose, 5–30 U/ml SLO for 10 min at 4°C. After removal of excess SLO, incubation was continued in the same buffer lacking SLO at 37°C for 30 min. Cells were observed under a Zeiss Axioplan microscope equipped for epifluorescence or with a Bio-Rad MRC 1024 ES laser confocal microscope.
Velocity Sucrose Gradient Centrifugation
CV1 cells transfected with wt b(5) in a 10-cm petri dish were washed free of medium with PBS, detached with a rubber policeman, sedimented, and resuspended in 200 μl of PBS and lysed for 10 min at 0°C with an equal volume of 2% Triton X-100, 40 mM NaCl, 50 mM Tris-Cl, pH 7.4, and protease inhibitors (2 mM phenylmethylsulfonyl fluoride, 1 μg/ml leupeptin, 1.4 μg/ml pepstatin, 2 μg/ml chymostatin) for 10 min on ice. A cleared lysate was obtained after centrifugation at 700 g for 10 min. The cleared lysate or a fraction of rat liver microsomes (1.3 mg of protein) solubilized under the same conditions as the cultured cells was loaded on top of a 12-ml 5–20% linear sucrose gradient containing 20 mM NaCl, 25 mM Tris-Cl, pH 7.4, 0.2% Triton X-100, in tubes of the SW40 rotor (Beckman Instruments, Inc.), and centrifuged at 39,000 rpm at 4°C for 16 h. Colored markers for sedimentation rates (cytochrome c and catalase) were run on a separate gradient centrifuged in parallel. 15 fractions were collected from the top with an Auto Densiflow probe (Buchler Instruments) and subjected to precipitation with TCA in the presence of 80 μg of cytochrome c as carrier. The precipitated proteins were analyzed by SDS-PAGE followed by Western blotting.
In Vitro Transcription and Translation
N-glyc and O-glyc b(5) in pGEM4 and a cDNA coding for the plant protein phaseolin cloned in pSP64T were transcribed from the SP6 promoter, and the resulting synthetic mRNA was translated for 1 h at 32°C in 10 or 20 μl of rabbit reticulocyte lysate (Promega Corp.) as described previously (Ceriotti et al. 1991 ), in the presence or absence of 1 μl of dog pancreas microsomes (Promega Corp.). In some samples, microsomes were added posttranslationally. In this case, the translation, carried out in the absence of microsomes, was stopped by addition of cycloheximide (CHX) (30 μg/ml), and elimination of ribosomes by centrifugation at 55,000 rpm for 1 h at 4°C in the Beckman TLA 100.3 rotor. The ribosome-free supernatants were then incubated for a further hour at 32°C in the presence of microsomes.
Metabolic Labeling Experiments
Metabolic labeling was carried out on CV1 or CHO15B cells, plated on 10-cm petri dishes, and transfected with b(5) or tagged versions thereof the day before exposure to the radioactive precursor. Labeling with 0.1–0.2 mCi/ml Met/Cys (Promix; Amersham Pharmacia Biotech) was carried out as described previously (Borgese et al. 1996 ). For labeling with high specific activity glucosamine (GlcNH2) or galactose (NEN Life Science Products or American Radiolabeled Chemicals, Inc.), cells were incubated for 1.5 h in MEM with Earle's salts containing glucose at reduced concentration (0.1 g/l) and 3% dialyzed FCS, before addition of the concentrated radioactive sugar to a final concentration of 0.3–0.6 mCi/ml. The length of the incubations, and the concentrations of added drugs (brefeldin A , okadaic acid , CHX; Sigma Chemical Co.) are specified in the figure legends.
Immunoprecipitation
Metabolically labeled cells were collected in PBS, lysed for 10 min at 0°C with an equal volume of 200 mM NaCl, 50 mM Tris-Cl, pH 7.4, 20 mM EDTA, 4% Triton X-100, and protease inhibitors. After clearing by centrifugation (1,000 g for 10 min), the lysates were analyzed for incorporation of the radioactive precursor and protein content. Aliquots of the lysates, containing equal amounts of incorporated radioactivity or equal amounts of protein, were precleared by incubation with protein A– or protein G–Sephrose beads in the presence of 0.2% gelatin, then incubated with anti-b(5) polyclonal Abs or antiopsin mAbs. The immune complexes were harvested with protein A– or protein G–Sepharose beads, in some cases treated with endoglycosidases, and finally analyzed by SDS-PAGE fluorography.
Cell Fractionation
Cell fractionation was carried out on cells plated on eight 10-cm petri dishes transfected with O-glyc b(5) and metabolically labeled with GlcNH2. All operations were carried out at 4°C. Cells were washed free of medium and detached with a rubber policeman. After collection by centrifugation, they were washed with homogenization solution (0.25 M sucrose, 0.5 mM EDTA, 0.5 mM EGTA, 20 mM Tris-Cl, pH 7.5, and protease inhibitors), resuspended in 1 ml of the same solution, and ruptured by eight passages through a cell cracker with a 0.0009-inch clearance. After elimination of nuclei by centrifugation (700 g for 10 min), the postnuclear supernatant (PNS) was brought to 27% wt/vol Optiprep (Nycomed), 20 mM tricine/NaOH, pH 7.8, 1.3% sucrose, and 1 mM EDTA, and layered under a linear 9.5-ml 8–22% isosmotic Optiprep gradient with the same ions as above. The gradients were topped with 0.3 ml of 8% sucrose plus ions, and centrifuged for 2 h at 28,000 rpm at 4°C in a Beckman SW41 rotor. Fractions were collected and equal aliquots were subjected to immunoprecipitation followed by SDS-PAGE fluorography or to Western blot analysis.
Biochemical Assays
Most of the techniques used in this study (SDS-PAGE, Western blotting, NADPH–cytochrome c enzyme assay) are described in previous publications (Borgese and Pietrini 1986 ; Borgese et al. 1996 ). Autoradiograms and fluorograms were scanned and band intensities determined using the NIH Image software.
For endoglycosidase (Endo) H treatment, immune complexes were detached from protein G–Sepharose beads by incubation for 3 min at 100°C in an equal volume of 40 mM Tris-Cl, pH 6.8, 4% SDS, 2% ?-mercaptoethanol, and 17% glycerol. After sedimentation of the beads, the supernatant was supplemented with five volumes of 0.1 M Na+ citrate buffer, pH 5.5, 0.6 μl of a 100-mg/ml solution of BSA and protease inhibitors, and then incubated overnight at 37°C with or without 10 mU of Endo H (Boehringer Mannheim). 5–10 μl of in vitro translation mix was similarly denatured and digested. For Endo D treatment, samples were denatured as for Endo H digestions, but the SDS-containing supernatants were diluted with five volumes of 0.25 M Na+phosphate, pH 7.2, 10 mM EDTA plus BSA, and protease inhibitors. Digestion was carried out overnight with 3 mU of Endo D (Boehringer Mannheim).
Results
Transmembrane Topology of b(5)
To plan a strategy for the investigation of the mechanism of residence of b(5) in the ER, it was first necessary to define the topology of the hydrophobic membrane-anchoring domain. Although b(5) is perhaps the first TA protein to have been characterized, there has been controversy as to whether it adopts a transmembrane disposition or whether it loops back into the cytosol. We investigated this problem with two different approaches as described below.
In the first approach, we used an Ab raised against the COOH terminus of b(5) (see Materials and Methods) to probe the accessibility of the COOH-terminal polar peptide by immunofluorescence in an MDCK cell line stably expressing b(5). Although this cell line originated from a single clone, only ~30% of the cells expressed detectable levels of b(5) at any one time. Cells were treated either with SLO to selectively permeabilize the plasma membrane (Bhakdi et al. 1993 ), or with Triton X-100 after fixation to permeabilize intracellular membranes. As shown in Fig 1, when the cells were permeabilized only with SLO, the cytosol became accessible to IgG, as demonstrated by the staining with antitubulin mAbs, which were equally effective with or without Triton X-100 permeabilization (compare Fig 1B and Fig D). In contrast, the ER lumen of SLO-permeabilized cells was poorly accessible, as demonstrated by the low (probably nonspecific) staining obtained with mAbs against the lumenal protein PDI (compare Fig 1F and Fig H). Under this same condition, the COOH terminus of b(5) was not accessible to Abs (Fig 1 A), which were, however, capable of binding their epitope after Triton X-100 treatment (Fig 1 C). In contrast to the anti–COOH-terminal peptide Ab, Abs raised against the catalytic domain of b(5) were able to bind the antigen regardless of the permeabilization protocol (Fig 1E and Fig G). The results illustrated in Fig 1 are evaluated quantitatively in Table 1, and are consistent with a lumenal location of the COOH-terminal polar peptide of b(5).
Table 1. Quantitative Analysis of b(5) Immunofluorescence in Transfected MDCK Cells Permeabilized with SLO or with SLO + Triton X-100
In the second approach, the COOH terminus of b(5) was extended with a sequence containing a consensus for N-glycosylation, as reporter for translocation into the ER lumen. The appended sequence (Fig 2 A) was derived from the NH2 terminus of bovine opsin. The resulting construct, N-glyc b(5), was translated in vitro under different conditions. As shown in the upper panel of Fig 2 B, lane 1, when N-glyc b(5) was translated in the presence of dog pancreas microsomes, two bands were obtained, of which one comigrated with the product obtained in the absence of membranes (lanes 3 and 4), and the other, indicated by the arrow, had a slower mobility and was Endo H–sensitive (lane 2), demonstrating that N-glyc b(5)'s COOH terminus is translocated across the membrane to become glycosylated. More importantly, if N-glyc b(5) was first translated, and microsomes that were added after translation were blocked by CHX, and ribosomes were removed by sedimentation, N-glyc b(5) was still glycosylated with high efficiency (lanes 5 and 6), demonstrating that the hydrophobic domain is capable of translocating downstream residues posttranslationally. As a control, we analyzed the behavior of phaseolin, a plant vacuolar glycoprotein that is translocated across the ER cotranslationally (Ceriotti et al. 1991 ). As shown in the lower panel of Fig 2 B, lane 1, phaseolin was modified to the mono- and diglycosylated forms (marked by one and two asterisks, respectively) when microsomes were present during translation, but remained unglycosylated when membranes were added after translation (lanes 5 and 6).
b(5) Overexpressed in CV1 Cells Is in the ER in a Nonaggregated State
In mammalian cells, the first station after exit from the ER is a tubular vesicular compartment, also known as an intermediate compartment (IC) (Bannykh and Balch 1997 ). Some proteins that are kept in the ER by a retrieval mechanism can be detected by immunofluorescence in the IC (Jackson et al. 1993 ; Martire et al. 1996 ; Lotti et al. 1999 ), and this IC localization can be increased by incubation at 15°C, a temperature that blocks exit from the IC (Jackson et al. 1993 ). We investigated whether this was also the case for b(5) by comparing its intracellular distribution with that of ERGIC 53, a marker for the IC (Schweizer et al. 1988 ), after incubation of transfected CV1 cells at 37 or 15°C. As can be seen in Fig 3b(5) could not be detected in structures enriched in ERGIC 53 either under normal incubation conditions (Fig 3, A–C), or after prolonged incubation at 15°C (Fig 3, D–F). Under the latter condition, ERGIC 53–containing elements clustered in the Golgi area (compare Fig 3E and Fig B) in agreement with the recent observations of Klumperman et al. 1998 . It should be mentioned that at longer times after transfection (>24 h), b(5) was often seen to concentrate in large structures that were positive for ER markers (see Fig 10). These structures may be related to the karmellae, which are induced in yeast cells by overexpression of b(5) (Vergeres et al. 1993 ). To avoid excessive formation of these structures, all the experiments described in this paper were initiated within 24 h after transfection.
Because a number of ER membrane proteins, including the ribophorins, are found in rapidly sedimenting aggregates after solubilization of microsomes with nonionic detergents, it is thought that in situ they form an intramembranous proteinaceous network, which could also be the basis for their retention in the ER (Yu et al. 1989 ). To investigate whether overexpressed b(5) might belong to such an aggregate, we analyzed its sedimentation on sucrose velocity gradients after detergent extraction from transfected CV1 cells and compared it with that of ribophorin I and of b(5) endogenous to rat liver microsomes. As can be seen from Fig 4, under the conditions used, ribophorin I extracted both from rat liver microsomes (Fig 4 A) and from transfected CV1 cells (Fig 4 B) formed rapidly sedimenting aggregates, in agreement with published work (Hortsch et al. 1986 ; Yu et al. 1989 ). In contrast, b(5) from rat liver microsomes or transfected CV1 cells was recovered in the upper fractions of the gradient, cosedimenting with cytochrome c as expected for the monomeric form of the protein (Mr ~15,000), suggesting that it exists in a freely diffusible form within the ER of the transfected cells.
Use of Tagged Versions of b(5) to Follow Its Intracellular Trafficking
To investigate with biochemical methodology whether b(5) is retrieved from a downstream compartment, we used COOH-terminally appended tags to report on the intracellular compartments visited by b(5) during its lifetime. In addition to N-glyc b(5) described above, we constructed a mutant with potential O-glycosylation sites at the COOH terminus (O-glyc b; Fig 2 A). The sequence chosen was derived from human glycophorin A (residues 35–48), followed by the sequence YTPPP, in which the Thr residue is in an optimal consensus for O-glycosylation (Yoshida et al. 1997 ).
We first checked by immunofluorescence whether the added tags altered the intracellular distribution of b(5) in transiently transfected CV1 cells. As shown in Fig 5, both polypeptides had a reticular distribution and a clear localization to the nuclear envelope, indicative of an ER localization. Moreover, like the wt protein, they were not concentrated in structures enriched in ERGIC 53, and their catalytic domain was accessible to Abs restricted to the cytosol, as demonstrated by the good reaction obtained in cells permeabilized only with SLO.
The Majority of N-glyc b(5) Does Not Reach the Compartment of Residence of Golgi Mannosidases I and II
To see whether the N-glycan of N-glyc b(5) is modified by mannosidase II, which is generally localized in the medial Golgi cisterna (Velasco et al. 1993 ), we investigated whether the metabolically labeled protein could acquire Endo H resistance. Cells were labeled with Met/Cys for 2 h, then chased for 6 h, and N-glyc b(5) was immunoprecipitated and analyzed by SDS-PAGE fluorography. As shown in Fig 6 A, lanes 1 and 2, after the 2 h pulse, most of the in vivo synthesized N-glyc b(5) was glycosylated and Endo H–sensitive; Endo H sensitivity was completely retained also after 6 h of chase (Fig 6 A, lanes 3 and 4). Since some N-linked glycans are not accessible to mannosidase II, even if they do transit through the Golgi, we checked whether the high mannose oligosaccharide attached to N-glyc b(5) could be modified by mannosidase II if forced into a common intracellular compartment. When cells were incubated with BFA to relocate Golgi enzymes to the ER (Lippincott-Schwartz et al. 1989 ), a portion of N-glyc b(5) was converted to a more slowly migrating Endo H–resistant polypeptide (Fig 6 A, lanes 5 and 6). We conclude that under normal conditions N-glyc b(5) does not reach the compartment of residence of mannosidase II.
An earlier step in N-glycan processing is trimming by mannosidase I, an event that can be monitored by assessing the acquisition of sensitivity to Endo D. We investigated the Endo D sensitivity of N-glyc b(5) in CHO 15B cells, which lack N-acetylglucosamine (GlcNac) transferase I activity, to avoid a possible loss of Endo D sensitivity by further processing in the Golgi. As shown in Fig 6 B, nearly all of the N-glyc b(5) remained Endo D–resistant after 6 h of chase (Fig 6 B, lanes 1 and 2). However, compared with the nondigested sample, a small increase in the amount of deglycoyslated polypeptide was visible after Endo D treatment (Fig 6 B, arrow), suggesting that a small proportion of the tagged b(5) may have had access to mannosidase I. After incubation with BFA, all of the N-glyc b(5) became Endo D–sensitive (Fig 6 B, lanes 3 and 4). These results indicate that the vast majority of N-glyc b(5) molecules do not reach the compartment of residence of mannosidase I during a 6-h chase.
Glycosylation of O-glyc b(5)
The results presented in Fig 6 indicate that N-glyc b(5) does not recycle through the medial Golgi; however, it was possible that it reaches an earlier Golgi subcompartment. To investigate this possibility, we turned to the O-glyc b(5) construct. The first step in O-glycosylation is attachment of an N-acetylgalactosamine (GalNac) residue to Thr or Ser residues, and the enzymes responsible for this reaction, the GalNac transferases, have been localized to the cis-Golgi as well as to more distal cisternae (Rottger et al. 1998 ).
We first compared the electrophoretic mobility of in vivo synthesized O-glyc b(5) with that of the in vitro generated primary translation product. As shown in Fig 7 A, the product expressed in transfected cells (Fig 7 A, lane 1) comigrated with the product synthesized in vitro in the absence (Fig 7 A, lane 2) or presence (Fig 7 A, lane 3) of membranes. However, if cells were incubated with BFA, O-glyc b(5) was shifted to a higher apparent Mr (compare Fig 7 B, lanes 3 and 4, or Fig 7 B, lanes 5 and 6), indicating that at least one of the potential O-glycosylation sites could be used if the protein came into contact with the relevant enzymes. To see whether in the absence of BFA the initial steps of O-glycosylation were also taking place but were not resulting in reduced electrophoretic mobility of O-glyc b(5), we carried out metabolic labeling experiments with 3H-labeled sugars. As shown in Fig 7 B, incubation with GlcNH2, which serves as precursor both to UDP-GlcNac and to UDP-GalNac, resulted in labeling of O-glyc b(5) both in the absence (Fig 7 B, lane 3) and the presence (Fig 7 B, lane 4) of BFA. The labeling was specific, because under the same conditions, wt b(5) was not labeled (Fig 7 B, lanes 1 and 2), although it was efficiently expressed, as shown by the Western blot in the lower part of Fig 7 B.
The second sugar to be added on O-linked oligosaccharides is galactose. With galactose as radioactive precursor, O-glyc b(5) became labeled in the presence of BFA (Fig 7 B, lane 6), and a weak signal was obtained also in the absence of the drug (Fig 7 B, lane 5). Thus, at steady-state, a small portion of the O-glyc mutant has also undergone the second step of O-glycosylation.
To investigate how rapidly glycosylation of O-glyc b(5) occurs after its synthesis, we followed the time course of incorporation of 3H-labeled sugar after blocking protein synthesis with CHX (Fig 8). Cells were first incubated for 3 h with GlcNH2 to allow for equilibration between UDP-GlcNac and UDP-GalNac. Incubation was then continued in the presence or absence of CHX. To control for the efficacy of the block in protein synthesis, a separate set of dishes of transfected cells was incubated in parallel with Met/Cys in the presence or absence of CHX, and O-glyc b(5) immunoprecipitates were then analyzed (Fig 8 B). CHX efficiently blocked the synthesis of O-glyc b(5) (Fig 8 B; compare lanes 2 and 4 with lanes 1 and 3). However, as shown in Fig 8 A and on the graph on the right side of Fig 8 C (obtained by normalizing the amount of immunoprecipitated 3H-labeled O-glyc b to the amount of O-glyc b expressed, as determined by Western blotting), the block in protein synthesis had no effect at all on the rate of sugar incorporation, which continued at a linear rate for 4 h after addition of the drug. This result stands in sharp contrast to the strong inhibitory effect of CHX on the incorporation of labeled sugar into total cellular proteins (graph on the left side of Fig 8 C). Thus, there is a large pool of unglycosylated O-glyc b(5) molecules that acquire O-linked sugar at a low rate. It should be mentioned that incubation with CHX for 4 h did not cause an appreciable decrease in the total amount of O-glyc b(5) or in the accumulation of the labeled species (compare Fig 8 A, lanes 4 and 5) in this and other experiments, indicating that under these conditions O-glyc b(5) is stable. The variations in the amounts sometimes detected in Western blots (e.g., Fig 8 A, lanes 3–5 vs. Fig 8 A, lanes 1 and 2) are presumably due to differences in transfection efficiencies in the different dishes.
The bulk of the available evidence indicates that the process of O-glycosylation occurs in the Golgi complex (Roth et al. 1994 ; Schweizer et al. 1994 ; Rottger et al. 1998 ). However, under some conditions, especially in infected cells, the initial steps may take place in a compartment upstream of the Golgi (discussed in Rottger et al. 1998 ). Moreover, recent evidence indicates that Golgi-resident enzymes slowly recycle through the ER (Cole et al. 1998 ; Storrie et al. 1998 ; Girod et al. 1999 ). To investigate whether O-glyc b(5) must leave the ER to become glycosylated, we treated cells with the phosphatase inhibitor OKA, a drug which blocks exit from the ER (Davidson et al. 1992 ; Pryde et al. 1998 ). Transfected cells were exposed to GlcNH2 for 3 h and then incubated further for another hour in the presence or absence of OKA. At this time cells were collected for biochemical analysis or analyzed by immunofluorescence. As shown in Fig 9 C, the intracellular localization of O-glyc b(5) (Fig 9 C, panels a and d) and of a Golgi marker (giantin; Fig 9 C, panels c and f) were unaffected by OKA. In contrast, ERGIC 53 was dispersed from the Golgi area to more peripherally located structures (compare Fig 9 C, panels e and b). These results are consistent with OKA's inhibition of ER-to-Golgi transport. At slightly later times of incubation, ERGIC 53 appeared uniformly distributed within the ER, but the cells began to suffer and to retract from the substrate (data not shown). Analysis by immunoprecipitation and Western blotting (Fig 9A and Fig B) showed a 3.2-fold increase in labeling of O-glyc b(5) between 3 and 4 h in the absence of OKA, and an ~50% inhibition of this increase by OKA. This is a fairly strong effect if one considers that OKA does not exert its full inhibitory activity immediately after addition (Davidson et al. 1992 ).
To exclude the possibility that OKA was decreasing O-glyc b(5) glycosylation through a direct or indirect inhibition of glycosyl transferases and not by a transport block, we analyzed its effect in the presence of BFA. As can be seen in Fig 9 A, the effect of OKA was reversed in the presence of BFA (Western blot; Fig 9 A, lanes 3 and 5). During a 1-h period of incubation with BFA, 41.7 ± 1.7% and 37.6 ± 1.6% (average ± half-range of two experiments) of O-glyc b(5) was converted to the slower migrating, fully processed form in the absence and presence of OKA, respectively.
Another important piece of information in Fig 9 can be obtained by examining the ratio of specific radioactivity (immunoprecipitate/Western) of O-glyc b(5) attained in the absence and presence of BFA (Fig 9 A, lanes 2 and 3). By scanning a lower exposure of fluorographs in which the bands labeled in the presence of BFA had not saturated the film (data not shown), we found that the specific radioactivity attained in 1 h by O-glyc b(5) in the absence of drugs was ~7% that attained by the lower Mr polypeptide of the doublet generated in the presence of BFA. Since the higher Mr band presumably contains additional labeled sugar, it could not be compared with the more rapidly migrating polypeptide. If one assumes that the lower Mr band of Fig 9 A, lane 3 is 100% glycosylated, this would indicate a half-time for glycosylation of O-glyc b(5) (in the absence of BFA) of ~10 h, in agreement with the slow acquisition of sugar after the blockade of protein synthesis demonstrated in Fig 8. This half-time may be an underestimate, since a fraction of the low Mr polypeptide molecules of Fig 9 A, lane 3 may be unglycosylated.
The results of Fig 9 suggest that O-glyc b(5) must leave the ER to become glycosylated. But does O-glyc b(5) return to its compartment of origin once it has exited? This question was investigated both by immunofluorescence and by cell fractionation (Fig 10). We carried out immunofluorescence analysis of transfected cells after long exposures (4 and 8 h) to CHX. From the data of Fig 8O-glyc b(5) acquires sugar linearly for up to 4 h in the presence of CHX, and on the basis of the estimate of 10 h for the half-time of O-glycosylation (Fig 9), ~25% of O-glyc b(5) molecules should have acquired sugar at this time. A concentration of these glycosylated molecules in the glycosylation compartment (cis-Golgi) should have been detectable by immunofluorescence. However, as shown in Fig 10 A, the tagged protein retained a similar distribution to that of the ER protein ribophorin I at 4 h of incubation (Fig 10 A, panels a–c), and did not colocalize with the Golgi marker giantin even after 8 h of incubation with CHX (Fig 10 A, panels d–f). Fig 10 A, panels a–c also show an example of the b(5)-rich structures that began to appear in some of the cells in this experiment (the arrowheads indicate two such structures). As shown in Fig 10 A, panels b and c, ribophorin I also localized to these structures, suggesting that they represent proliferations of the ER. The frequency of these structures was, in any case, the same in cells incubated with or without CHX (data not shown).
The subcellular localization of glycosylated O-glyc b(5) was also analyzed by Optiprep density gradient centrifugation of a PNS from cells metabolically labeled with GlcNH2 (Fig 10 B). Under the conditions used, the ER marker NADPH-cyt P450 reductase showed a sharp peak of activity centered at fraction 6, corresponding to a density of 1.1 (Fig 10 B, panel b), whereas GS28, a marker for the cis-Golgi (Subramaniam et al. 1995 ), was broadly distributed throughout the gradient and present also in the bottom fractions immediately adjacent to the load zone (Fig 10 B, panel d). Total O-glyc b(5), detected by Western blot (Fig 10 B, panel a), peaked at a slightly lower density (fraction 5) than the reductase. A portion of O-glyc b(5) floated to the top of the gradient. This material probably corresponds to membrane fragments of low density, which we have not characterized further. Finally, 3H-labeled O-glyc b(5), detected by immunoprecipitation (Fig 10 B, panel c), had a distribution similar to that of total O-glyc b(5), and was depleted from the region of the gradient more enriched in GS28 (fractions 7–9). These results suggest that unglycosylated and glycosylated O-glyc b(5) molecules coexist within the same compartment, and also that both may be enriched in smooth subdomains of the ER.
Discussion
Both retention and retrieval mechanisms are thought to be involved in keeping ER resident proteins from escaping down the secretory pathway. The identification of specific retrieval sequences has spurred a large amount of work that has resulted in a significant increase in our understanding of the retrograde pathway (Pelham and Munro 1993 ; Cosson and Letourneur 1994 ; Teasdale and Jackson 1996 ; Cosson et al. 1998 ). However, most of this work has been carried out on chimeras, consisting of a retrieval signal grafted onto a protein normally destined for export from the ER, and there is still not much information on the relative roles of retention and retrieval in determining the residence of bona fide ER proteins. A few mammalian ER membrane proteins have been studied by analyzing the processing of N-linked glycans attached to endogenous or engineered consensus sites. Due the failure of these proteins to acquire Endo H resistance, it has been concluded that they reside in the ER by a true retention mechanism (Ahn et al. 1993 ; Masaki et al. 1996 ; Duvet et al. 1998 ; Honsho et al. 1998 ). However, since Endo H resistance is acquired in the medial Golgi, these studies could not exclude that retrieval from an earlier Golgi compartment was occurring. In this study, we have addressed this problem by attaching short sequences, containing either N- or O-glycosylation sites, to the COOH terminus of b(5), a TA protein of the ER. We show that in the O-glyc mutant at least one glycosylation site is used, indicating that the tagged protein comes in contact with cis-Golgi enzymes, an event which could not be detected by analysis of the oligosaccharide of the N-glyc–tagged version. The methodology used here should also be useful for the study of the trafficking of other ER membrane proteins, particularly of those lacking lumenal domains with endogenous glycosylation sites.
Posttranslational Translocation of the COOH Terminus of b(5) across the ER Membrane
Before undertaking an investigation of the intracellular sorting of b(5), we judged it necessary to define the topology of its membrane-anchoring domain. Although this problem has been the object of numerous investigations, there were still conflicting views as to whether b(5)'s hydrophobic domain adopts a transmembrane disposition with the extreme COOH-terminal residues in the lumen of the ER, or whether it has a hairpin topology with the COOH terminus looping back into the cytosol (Dailey and Strittmatter 1981 ; Arinc et al. 1987 ; Ozols 1989 ; Chester et al. 1992 ; Borgese et al. 1993 ; Vergeres et al. 1995 ; Kuroda et al. 1996 ). However, strong evidence for a transmembrane topology for b(5) was provided recently by the finding that a tagged version bearing an N-glycosylation consensus sequence at the COOH terminus acquired N-linked carbohydrate (Honsho et al. 1998 ). Although this study proved that the COOH terminus of this construct is translocated into the ER lumen in vivo, it did not investigate the mechanism of this translocation, leaving open the possibility that the addition of polar residues at the COOH terminus could cause a translocation that does not occur with the wt, untagged polypeptide. For instance, the additional 15–20 COOH-terminal amino acids could lead to a partial exposure of residues of the hydrophobic domain before termination of translation, resulting in the binding of the signal recognition particle and in a translocon-dependent translocation. For this reason, and since the wt protein is synthesized on free polysomes and inserts into membranes after release from the ribosomes, it was important to establish that the translocation of the COOH terminus of COOH-terminally tagged b(5) could occur posttranslationally in the absence of ribosomes. Our results with the N-glyc b(5) mutant show that this is indeed the case, a strong indication that in the wt protein the seven polar COOH-terminal residues are also in the lumen of the ER. In agreement with this conclusion, in immunofluorescence experiments we found that the COOH-terminal polar peptide is not accessible to Abs unless the ER membrane is permeabilized with Triton X-100. Taken together these results justify the use of COOH-terminally tagged versions of b(5) to study its intracellular trafficking.
Although the hydrophobic domain of b(5), in its ability to translocate downstream residues across the ER membrane, superficially resembles the signal anchor sequences of classical type II proteins, the mechanism by which it functions is quite different, since it operates on the released polypeptide in the absence of ribosomes. An in vitro posttranslational translocation similar to that of the b(5) COOH terminus has been shown also for synaptobrevin I (Kutay et al. 1995 ), a synaptic vesicle soluble N-ethylmaleimide–sensitive factor attachment protein receptor with a considerably longer hydrophobic domain than b(5). The insertion of synaptobrevin appeared to require proteins different from those of the classical Sec61-based translocation apparatus. It is likely that b(5) and synaptobrevin, as well as all other TA proteins, translocate their COOH terminus with the same mechanism, which certainly deserves further investigation.
Retention or Retrieval?
To investigate whether b(5) is retrieved from the IC or from the cis-Golgi, we first compared its distribution by immunofluorescence with that of the IC marker, ERGIC 53, after incubation either under normal conditions or at 15°C, a temperature which interferes with trafficking between the ER and the Golgi, and which has been shown in some cases to cause accumulation of recycling ER proteins in the IC (Jackson et al. 1993 ). However, for b(5), this approach did not yield any evidence in favor of its movement out of the ER. Proteins that recycle slowly may not be captured in the IC by incubation at low temperature (Jackson et al. 1993 ), presumably because entry as well as exit from the IC may be slowed. Therefore, we turned to the use of lumenally tagged versions of b(5) (N-glyc and O-glyc b), with the aim of using the attached oligosaccharide chains as reporters for the intracellular compartments visited by b(5). These tagged constructs were inserted into membranes with the correct topology, and had an intracellular distribution indistinguishable from that of transiently expressed wt b(5). During a 6-h chase, N-glyc b(5) did not acquire Endo H resistance, and also remained nearly completely Endo D–resistant, suggesting that it was not reaching the medial Golgi. However, when we turned to a more stringent assay based on the incorporation of sugar into the O-glyc mutant, we found that at least one O-glycosylation site was used, indicating that the protein was coming into contact with a GalNac transferase, enzymes which are localized to the Golgi complex (Rottger et al. 1998 ). We believe that the acquisition of carbohydrate by O-glyc b(5) is reporting on a recycling event through the cis-Golgi, for the reasons detailed below.
Processing of a glycoprotein by Golgi enzymes has normally been taken as evidence for its passage though the Golgi complex. However, recent evidence showing that Golgi enzymes recycle slowly through the ER (Cole et al. 1998 ; Storrie et al. 1998 ; Girod et al. 1999 ) makes it more difficult to interpret the significance of Golgi modifications on ER proteins. Nonetheless, since ER proteins generally do not carry Golgi modifications, it seems that these recycling Golgi enzymes are not active within the ER. Therefore, it is probable that O-glyc b(5) acquired its sugar after leaving the ER, and this idea is supported by the finding that glycosylation of O-glyc b(5) could be inhibited by the phosphatase inhibitor OKA, which blocks transport out of the ER (Davidson et al. 1992 ; Pryde et al. 1998 ). If O-glyc b(5) had been modified within the ER by recycling Golgi enzymes, OKA might actually have increased the processing of O-glyc b(5) by the trapped glycosyl transferases. Another explanation for our data is that the tagged protein, after exiting the ER and becoming glycosylated, did not return to its compartment of origin. This interpretation is unlikely, since no redistribution of O-glyc b(5) from the ER to another compartment could be observed after a chase with CHX under conditions in which the proportion of glycosylated O-glyc b(5) molecules was increasing at a linear rate. Moreover, GlcNH2-labeled and total O-glyc b(5) had similar distributions on an Optiprep density gradient, suggesting that they coexist in the same intracellular compartment.
Does the behavior of overexpressed O-glyc b(5) reflect that of endogenous b(5) in mammalian cells? It is possible that overexpression causes leakage from the ER of the tagged b(5) or that the tag itself alters the behavior of b(5). Although we cannot exclude either of these possibilities, the important finding here is that b(5) appears to have the capacity to be captured and returned to the ER from a downstream compartment, even though the extent of exit from the ER for the endogenous molecule and the overexpressed tagged mutant may be different. The rate of acquisition of carbohydrate by O-glyc b(5) was in any case quite slow: by comparing the extent of labeling of the tagged protein in the presence or absence of BFA, we estimated a half-time for acquisition of O-linked GalNac of ~10 h. This slow rate of glycosylation, as well as the lack of colocalization of wt and tagged versions of b(5) with markers for the IC, suggest that b(5) tends to be excluded from budding transport vesicles, and that retrieval from a downstream compartment represents a salvage mechanism for those molecules that occasionally leak out of the ER. In other words, it would appear that both retention and retrieval are operating together to keep b(5) in the ER. We do not know at present whether retention is based simply on the lack of a positive export signal and/or the presence of a positive retention signal or feature in b(5). Formation of oligomeric complexes has been suggested to result in retention of some ER proteins (Yu et al. 1989 ). However, this mechanism would not seem to be responsible for b(5) retention. Indeed, our sucrose gradient analysis did not reveal the presence of b(5) oligomers under conditions in which high-Mr complexes containing ribophorin I were preserved. Consistent with this result, preliminary experiments carried out with the fluorescence recovery after photobleaching technique suggest that green fluorescent protein–b(5) chimeras diffuse rapidly across the ER (Snapp, E., and J. Lippincott-Schwartz, personal communication).
Our previous work demonstrated that a short hydrophobic domain is required to keep b(5) in the ER; lengthening of the TMD results in escape of b(5) from the ER and its arrival at the plasma membrane (Pedrazzini et al. 1996 ). The extension of this finding by other laboratories to other TA proteins and reporter constructs (Rayner and Pelham 1997 ; Yang et al. 1997 ; Honsho et al. 1998 ) suggests that TMD-dependent sorting may be a general phenomenon for TA proteins and may occur by a common mechanism. The results of the present study, which suggest that both retention and retrieval mechanisms are operating to keep b(5) in the ER, raise the question as to whether the short TMD is required for retention, retrieval, or for both these phenomena. If the TMD is involved in retrieval, a candidate recycling receptor involved in this process is rer1p, a protein demonstrated to be required for ER residence of a number of membrane polypeptides in yeast via recognition of their TMDs (Sato et al. 1996 , Sato et al. 1997 ). This receptor, which also has been cloned from mammalian cells (Fullekrug et al. 1997 ), appears to prefer short and somewhat hydrophilic TMDs (Letourneur and Cosson 1998 ). On the other hand, retrieval of TA proteins may occur by a completely different mechanism, since Ufe1p, a TA target soluble N-ethylmaleimide–sensitive factor attachment protein receptor of the ER, does not change its localization in rer1p-deficient yeast cells (Rayner and Pelham 1997 ). Further work with tagged versions of TA proteins like the ones described in this study should help to define at the molecular level the sorting mechanisms of this class of proteins.
References
Adamus, G., Arendt, A., Hargrave, P.A. 1991. Genetic control of antibody response to bovine rhodopsin in mice: epitope mapping of rhodopsin structure. J. Neuroimmunol. 34:89-97.
Ahn, K., Szczesna-Skorupa, E., Kemper, B. 1993. The amino-terminal 29 amino acids of cytochrome P450 2C1 are sufficient for retention in the endoplasmic reticulum. J. Biol. Chem. 268:18726-18733.
Arinc, E., Rzepecki, L.M., Strittmatter, P. 1987. Topography of the C-terminus of cytochrome b5 tightly bound to dimyristoylphosphatidylcholine vesicles. J. Biol. Chem. 262:15563-15567.
Bannykh, S.I., Balch, W.E. 1997. Membrane dynamics at the endoplasmic reticulum-Golgi interface. J. Cell Biol. 138:1-4.
Bhakdi, S., Weller, U., Walev, I., Martin, E., Jonas, D., Palmer, M. 1993. A guide to the use of pore-forming toxins for controlled permeabilization of cell membranes. Med. Microbiol. Immunol. 182:167-175.
Borgese, N., Meldolesi, J. 1976. Immunological similarity of the NADH-cytochrome c electron transport system in microsomes, Golgi complex and mitochondrial outer membrane of rat liver cells. FEBS Lett. 63:231-234.
Borgese, N., Pietrini, G. 1986. Distribution of the integral membrane protein NADH-cytochrome b5 reductase in rat liver cells, studied with a quantitative radioimmunoblotting assay. Biochem. J. 239:393-403.
Borgese, N., D'Arrigo, A., De Silvestris, M., Pietrini, G. 1993. NADH-cytochrome b5 reductase and cytochrome b5—the problem of posttranslational targeting to the endoplasmic reticulum. In Borgese N., Harris J.R., eds. Subcellular Biochemistry. Vol. 21. New York, Plenum Press, 313-341.
Borgese, N., Aggujaro, D., Carrera, P., Pietrini, G., Bassetti, M. 1996. A role for N-myristoylation in protein targeting: NADH-cytochrome b5 reductase requires myristic acid for association with outer mitochondrial but not endoplasmic reticulum membranes. J. Cell Biol. 135:1501-1513.
Brewer, C.B., Roth, M.G. 1991. A single amino acid change in the cytoplasmic domain alters the polarized delivery of influenza virus hemagglutinin. J. Cell Biol. 114:413-421.
Ceriotti, A., Pedrazzini, E., Fabbrini, M.S., Zoppè, M., Bollini, R., Vitale, A. 1991. Expression of the wild-type and mutated vacuolar storage protein phaseolin in Xenopus oocytes reveals relationships between assembly and intracellular transport. Eur. J. Biochem. 202:959-968.
Chester, D.W., Skita, V., Young, H.S., Mavromoustakos, T., Strittmatter, P. 1992. Bilayer structure and physical dynamics of the cytochrome b(5) dimyristoylphosphatidylcholine interaction. Biophys. J. 61:1224-1243.
Cole, N.B., Ellenberg, J., Song, J., DiEuliis, D., Lippincott-Schwartz, J. 1998. Retrograde transport of Golgi-localized proteins to the ER. J. Cell Biol. 140:1-15.
Cosson, P., Letourneur, F. 1994. Coatomer interaction with di-lysine endoplasmic reticulum retention motifs. Science. 263:1629-1631.
Cosson, P., Lefkir, Y., Démollière, C., Letourneur, F. 1998. New COP1-binding motifs involved in ER retrieval. EMBO (Eur. Mol. Biol. Organ.) J. 17:6863-6870.
Dailey, H.A., Strittmatter, P. 1981. Orientation of the carboxyl and NH2 termini of the membrane-binding segment of cytochrome b5 on the same side of phospholipid bilayers. J. Biol. Chem. 256:3951-3955.
Davidson, H.W., McGowan, C.H., Balch, W.E. 1992. Evidence for the regulation of exocytic transport by protein phosphorylation. J. Cell Biol. 116:1343-1355.
De Silvestris, M., D'Arrigo, A., Borgese, N. 1995. The targeting information of the mitochondrial outer membrane isoform of cytochrome b5 is contained within the carboxyl-terminal region. FEBS Lett. 370:69-74.
Duvet, S., Cocquerel, L., Pillez, A., Cacan, R., Verbert, A., Moradpour, D., Wychowski, C., Dubuisson, J. 1998. Hepatitis C virus glycoprotein complex localization in the endoplasmic reticulum involves a determinant for retention and not retrieval. J. Biol. Chem. 273:32088-32095.
Fullekrug, J., Boehm, J., Rottger, S., Nilsson, T., Mieskes, G., Schmitt, H.D. 1997. Human Rer1 is localized to the Golgi apparatus and complements the deletion of the homologous Rer1 protein of Saccharomyces cerevisiae. Eur. J. Cell Biol. 74:31-40.
Giordano, S.J., Steggles, A.W. 1992. Identification and nucleotide sequence of the leukocyte and reticulocyte forms of rabbit cytochrome b5 mRNA. SAAS Bull. Biochem. Biotechnol. 5:13-17.
Girod, A., Storrie, B., Simpson, J.C., Johannes, L., Goud, B., Roberts, L.M., Lord, J.M., Nilsson, T., Pepperkok, R. 1999. Evidence for a COP-I-independent transport route from the Golgi complex to the endoplasmic reticulum. Nat. Cell Biol. 1:423-430.
Honsho, M., Mitoma, J., Ito, A. 1998. Retention of cytochrome b(5) in the endoplasmic reticulum is transmembrane and luminal domain-dependent. J. Biol. Chem. 273:20860-20866.
Hortsch, M., Avossa, D., Meyer, D.I. 1986. Characterization of secretory protein translocation: ribosome-membrane interaction in endoplasmic reticulum. J. Cell Biol. 103:241-253.
Jackson, M.R., Nilsson, T., Peterson, P.A. 1993. Retrieval of transmembrane proteins to the endoplasmic reticulum. J. Cell Biol. 121:317-333.
Klumperman, J., Schweizer, A., Clausen, H., Tang, B.L., Hong, W., Oorschot, V., Hauri, H.-P. 1998. The recycling pathway of protein ERGIC-53 and dynamics of the ER-Golgi intermediate compartment. J. Cell Sci. 111:3411-3425.
Kuroda, R., Kinoshita, J., Honsho, M., Mitoma, J., Ito, A. 1996. In situ topology of cytochrome b(5) in the endoplasmic reticulum membrane. J. Biochem. (Tokyo). 120:828-833.
Kutay, U., Hartmann, E., Rapoport, T.A. 1993. A class of membrane proteins with C-terminal anchor. Trends Cell Biol. 3:72-75.
Kutay, U., Ahnert-Hilgen, G., Hartmann, E., Wiedenmann, B., Rapoport, T.A. 1995. Transport route for synaptobrevin via a novel pathway of insertion into the endoplasmic reticulum membrane. EMBO (Eur. Mol. Biol. Organ.) J. 14:224-231.
Letourneur, F., Cosson, P. 1998. Targeting to the endoplasmic reticulum in yeast cells by determinants present in transmembrane domains. J. Biol. Chem. 273:33273-33278.
Lippincott-Schwartz, J., Yuan, L.C., Bonifacino, J.S., Klausner, R.D. 1989. Rapid redistribution of Golgi proteins into the ER in cells treated with brefeldin A: evidence for membrane cycling from Golgi to ER. Cell. 56:801-813.
Lotti, L.V., Mottola, G., Torrisi, M.R., Bonatti, S. 1999. A different intracellular distribution of a single reporter protein is determined at steady state by KKXX or KDEL retrieval signals. J. Biol. Chem. 274:10413-10420.
Martire, G., Mottola, G., Pascale, M.C., Malagolini, N., Turrini, I., Serafini-Cessi, F., Jackson, M.R., Bonatti, S. 1996. Different fate of a single reporter protein containing KDEL or KKXX targeting signals stably expressed in mammalian cells. J. Biol. Chem. 271:3541-3547.
Masaki, R., Yamamoto, A., Tashiro, Y. 1996. Membrane topology and retention of microsomal aldehyde dehydrogenase in the endoplasmic reticulum. J. Biol. Chem. 271:16939-16944.
Nicchitta, C.V., Migliaccio, G., Blobel, G. 1991. Biochemical fractionation and assembly of the membrane components that mediate nascent chain targeting and translocation. Cell. 65:587-598.
Ozols, J. 1989. Structure of cytochrome b(5) and its topology in the microsomal membrane. Biochim. Biophys. Acta. 997:121-130.
Park, S.S., Walker, W., Aoyama, T., Lapenson, D.P., Waxman, D.J., Gonzales, F.J., Gelboin, H.V. 1992. Monoclonal antibodies to rat liver microsomal cytochrome b5. Biochem. Pharmacol. 43:2201-2208.
Pedrazzini, E., Villa, A., Borgese, N. 1996. A mutant cytochrome b5 with a lengthened membrane anchor escapes from the endoplasmic reticulum and reaches the plasma membrane. Proc. Natl. Acad. Sci. USA. 93:4207-4212.
Pelham, H.R.B., Munro, S. 1993. Sorting of membrane proteins in the secretory pathway. Cell. 75:603-605.
Pryde, J.G., Farmaki, T., Lucocq, J.M. 1998. Okadaic acid induces selective arrest of protein transport in the rough endoplasmic reticulum and prevents export into COPII-coated structures. Mol. Cell. Biol. 18:1125-1135.
Rayner, J.C., Pelham, H.R.B. 1997. Transmembrane domain-dependent sorting of proteins to the ER and plasma membrane in yeast. EMBO (Eur. Mol. Biol. Organ.) J. 16:1832-1841.
Roth, J., Wang, Y., Eckhardt, A.E., Hill, R.L. 1994. Subcellular localization of the UDP-N-acetyl-D-galactosamine: polypeptide N-acetylgalactosaminyltransferase-mediated O-glycosylation reaction in the submaxillary gland. Proc. Natl. Acad. Sci. USA. 91:8935-8939.
R?ttger, S., White, J., Wandall, H.H., Olivo, J.-C., Stark, A., Bennett, E.P., Whitehouse, C., Berger, E.G., Clausen, H., Nilsson, T. 1998. Localization of three human polypeptide GalNAc-transferases in HeLa cells suggests initiation of O-linked glycosylation throughout the Golgi apparatus. J. Cell Sci. 111:45-60.
Sato, K., Sato, M., Nakano, A. 1997. Rer1p as common machinery for the endoplasmic reticulum localization of membrane proteins. Proc. Natl. Acad. Sci. USA. 94:9693-9698.
Sato, M., Sato, K., Nakano, A. 1996. Endoplasmic reticulum localization of Sec12p is achieved by two mechanisms: Rer1p-dependent retrieval that requires the transmembrane domain and Rer1p-independent retention that involves the cytoplasmic domain. J. Cell Biol. 134:279-293.
Schweizer, A., Fransen, J.A.M., Bachi, T., Ginsel, L., Hauri, H.-P. 1988. Identification, by a monoclonal antibody, of a 53-kD protein associated with a tubulo-vesicular compartment at the cis-side of the Golgi apparatus. J. Cell Biol. 107:1643-1653.
Schweizer, A., Clausen, H., van Meer, G., Hauri, H.-P. 1994. Localization of O-glycan initiation, sphingomyelin synthesis, and glycosylceramide synthesis in Vero cells with respect to the endoplasmic reticulum-Golgi intermediate compartment. J. Biol. Chem. 269:4035-4041.
Seelig, H.P., Schranz, P., Schr?ter, H., Wiemann, C., Renz, M. 1994. Macrogolgin—a new 376 kD Golgi complex outer membrane protein as target of antibodies in patients with rheumatic disease and HIV infections. J. Autoimmun. 7:67-91.
Sonnichsen, B., Fullekrug, J., Nguyen Van, P., Diekmann, W., Robinson, D.G., Mieskes, G. 1994. Retention and retrieval: both mechanisms cooperate to maintain calreticulin in the endoplasmic reticulum. J. Cell Sci. 107:2705-2717.
Springer, S., Spang, A., Schekman, R. 1999. A primer on vesicle budding. Cell. 97:145-148.
Storrie, B., White, J., Rottger, S., Stelzer, E.H.K., Sugunuma, T., Nilsson, T. 1998. Recycling of Golgi-resident glycosyltransferases through the ER reveals a novel pathway and provides an explanation for nocodazole-induced Golgi scattering. J. Cell Biol. 143:1505-1521.
Subramaniam, V.N., Krijnse-Locker, J., Tang, B.L., Ericsson, M., Yusoff, A.R., Griffiths, G., Hong, W. 1995. Monoclonal antibody HFD9 identifies a novel 28 kD integral membrane protein on the cis-Golgi. J. Cell Sci. 108:2405-2414.
Teasdale, R.D., Jackson, M.R. 1996. Signal-mediated sorting of membrane proteins between the endoplasmic reticulum and the Golgi apparatus. Annu. Rev. Cell Dev. Biol. 12:27-54.
Tomita, M., Marchesi, V.T. 1975. Amino-acid sequence and oligosaccharide attachment sites of human erythrocyte glycophorin. Proc. Natl. Acad. Sci. USA. 72:2964-2968.
Velasco, A., Hendricks, L., Moremen, K.W., Tulsiani, D.R., Touster, O., Farquhar, M.G. 1993. Cell type-dependent variations in the subcellular distribution of alpha-mannosidase I and II. J. Cell Biol. 122:39-51.
Vergères, G., Yen, T.S., Aggeler, J., Lausier, J., Waskell, L. 1993. A model system for studying membrane biogenesis. Overexpression of cytochrome b5 in yeast results in marked proliferation of the intracellular membrane. J. Cell Sci. 106:249-259.
Vergères, G., Ramsden, J., Waskell, L. 1995. The carboxyl terminus of the membrane-binding domain of cytochrome b5 spans the bilayer of the endoplasmic reticulum. J. Biol. Chem. 270:3414-3422.
Yang, M., Ellenberg, J., Bonifacino, J.S., Weissman, A.M. 1997. The transmembrane domain of a carboxyl-terminal anchored protein determines localization to the endoplasmic reticulum. J. Biol. Chem. 272:1970-1975.
Yoshida, A., Suzuki, M., Ikenaga, H., Takeuchi, M. 1997. Discovery of the shortest sequence motif for high level mucin-type O-glycosylation. J. Biol. Chem. 272:16884-16888.
Yu, Y., Zhang, Y., Sabatini, D.D., Kreibich, G. 1989. Reconstitution of translocation-competent membrane vesicles from detergent-solubilized dog pancreas rough microsomes. Proc. Natl. Acad. Sci. USA. 86:9931-9935.
Yu, Y., Sabatini, D.D., Kreibich, G. 1990. Antiribophorin antibodies inhibit the targeting to the ER membrane of ribosomes containing nascent secretory polypeptides. J. Cell Biol. 111:1335-1342.(Emanuela Pedrazzinia, Antonello Villaa,b)
b Biological and Technological Research Department, Scientific Institute San Raffaele, Milan, Italy 20132
c Consiglio Nazionale Ricerche Institute of Biocatalysis and Molecular Recognition, Milan, Italy 20133
d Faculty of Pharmacy, University of Catanzaro "Magna Graecia", Roccelletta di Borgia (Catanzaro), Italy 88021
Correspondence to: Nica Borgese, Consiglio Nazionale Ricerche Cellular and Molecular Pharmacology Center, via Vanvitelli 32, 20129 Milan, Italy. Tel:39-02-7014-6250 Fax:39-02-7490-574 E-mail:nica@farma.csfic.mi.cnr.it.
Abstract
Endoplasmic reticulum (ER) proteins maintain their residency by static retention, dynamic retrieval, or a combination of the two. Tail-anchored proteins that contain a cytosolic domain associated with the lipid bilayer via a hydrophobic stretch close to the COOH terminus are sorted within the secretory pathway by largely unknown mechanisms. Here, we have investigated the mode of insertion in the bilayer and the intracellular trafficking of cytochrome b(5) (b), taken as a model for ER-resident tail-anchored proteins. We first demonstrated that b(5) can acquire a transmembrane topology posttranslationally, and then used two tagged versions of b(5), N-glyc and O-glyc b(5), containing potential N- and O-glycosylation sites, respectively, at the COOH-terminal lumenal extremity, to discriminate between retention and retrieval mechanisms. Whereas the N-linked oligosaccharide provided no evidence for retrieval from a downstream compartment, a more stringent assay based on carbohydrate acquisition by O-glyc b(5) showed that b(5) gains access to enzymes catalyzing the first steps of O-glycosylation. These results suggest that b(5) slowly recycles between the ER and the cis-Golgi complex and that dynamic retrieval as well as retention are involved in sorting of tail-anchored proteins.
Key Words: cell compartmentation, endoplasmic reticulum, glycosylation, Golgi apparatus, membrane proteins
Introduction
Notwithstanding the intense membrane traffic taking place within eukaryotic cells, subcellular compartments maintain their molecular identity with remarkable accuracy. Within the secretory pathway, proteins that reside in a given compartment must avoid being relocated to neighboring compartments in the face of ongoing transport. Two different mechanisms, static retention and dynamic retrieval, can, in principle, ensure that each compartment keeps its cohort of resident proteins. Retained proteins are thought to be simply excluded from transport out of their compartment of residence, whereas retrieved proteins do escape to a downstream organelle from which they are recycled by retrograde transport (Pelham and Munro 1993 ).
Consistent with its diverse functions, the membrane of the ER has a complex molecular composition, and many studies have been devoted to the mechanisms through which it keeps its numerous resident polypeptides from following transported proteins down the secretory pathway. These studies have shown that both retrieval via coat protein I–coated vesicles and retention are operative in determining residence of ER membrane proteins (for review see Teasdale and Jackson 1996 ). Of the two mechanisms, the former is better understood, and retrieval signals have been identified in the cytosolic tails of type I and type II ER resident membrane proteins (Cosson and Letourneur 1994 ; Teasdale and Jackson 1996 ; Cosson et al. 1998 ). In addition, a number of membrane proteins are retrieved by interaction of their transmembrane domains (TMDs)1 with a recently identified receptor, rer1p (Sato et al. 1996 , Sato et al. 1997 ). Less information is available on static retention. Although it could be argued that retention is effected simply by the absence of positive signals required for efficient recruitment of cargo protein into transport vesicles (Springer et al. 1999 ), it is likely that specific retention signals or features are also necessary to prevent access of retained proteins into budding vesicles (Sonnichsen et al. 1994 ).
Although there is evidence that both retrieval and retention operate at the ER–Golgi complex boundary, an important question that is still largely unresolved are the relative roles played by these two mechanisms in determining the residency of ER membrane proteins. Posttranslational modifications are generally used to follow intracellular trafficking between the ER and the Golgi. However, many ER membrane proteins do not have consensus sites for such modifications and are thus difficult to study. For instance, membrane proteins with the so-called tail-anchored (TA) topology, consisting of an NH2-terminal active cytosolic domain and a hydrophobic membrane-anchoring region close to the COOH terminus, essentially lack a lumenal domain (for reviews see Borgese et al. 1993 ; Kutay et al. 1993 ). Many ER enzymes whose catalytic activity is at the cytosolic side of the membrane have a TA topology, e.g., cytochrome b(5) (b), heme oxygenase, aldehyde dehydrogenase, and ubiquitin conjugating enzyme 6, and unraveling their sorting mechanisms would make an important contribution to our understanding of the genesis and maintenance of the molecular identity of the ER. In our laboratory we have been using b(5) as a model to study the targeting and sorting of ER-resident TA proteins. b(5) is an ~15,000-Mr protein with an NH2-terminal, globular cytosolic heme-binding domain, a short connecting region, and a hydrophobic anchoring domain followed by seven polar residues at the extreme COOH terminus (for review see Borgese et al. 1993 ). Since ER-resident TA enzymes generally have short hydrophobic anchoring domains (14–18 residues), we investigated a possible role of the length of the hydrophobic domain in sorting and demonstrated that a short anchoring domain is required to keep b(5) from escaping from the ER and from travelling down the secretory pathway to the cell surface (Pedrazzini et al. 1996 ). A similar observation was subsequently made on other ER-resident TA proteins (Rayner and Pelham 1997 ; Yang et al. 1997 ), establishing the generality of tail length–dependent sorting. However, an open question remained as to whether the short hydrophobic domain effects ER residence of TA proteins by a static retention or by a dynamic retrieval mechanism. In this study, we have investigated this question. Using tagged versions of b(5) with N- or O-glycosylation sites attached at the COOH terminus, we show that b(5) gains access to enzymes catalyzing the first steps of O-glycosylation, suggesting that it slowly recycles between the ER and the cis-Golgi.
Materials and Methods
Plasmid Constructions
A cDNA coding for the rabbit ER form of b(5) (Giordano and Steggles 1992 ) and subcloned into pGEM 4 and into the mammalian expression vector pCB6 (Brewer and Roth 1991 ), has been described in previous work (Pedrazzini et al. 1996 ). We refer to the protein expressed from this plasmid as wild-type (wt) b(5).
To facilitate addition of sequence tags at the COOH terminus of b(5), we introduced a unique Age1 site at the border between the hydrophobic domain and the extreme COOH-terminal polar region, which did not alter the encoded amino acid sequence, and Xba1 and Hind3 sites immediately after the stop codon. The three restriction sites were introduced by substituting a 3' terminal Aat2-Hind3 620-bp fragment of wt b(5) in pGEM4 (the Aat2 site at position 335 and the Hind3 site in the polylinker) with a 214-bp, PCR-generated fragment. The resulting plasmid (pGbAX) was used to construct the N-glyc b(5) and O-glyc b(5) mutants, which contained, close to their COOH termini, potential N- and O-glycosylation sites, respectively. The 25-bp Age1-Xba1 fragment of pGb(5)AX was replaced with an 89-bp duplex or 86-bp duplex obtained by annealing two complementary synthetic oligonucleotides coding for the sequences illustrated in Fig 2 A. The constructs were checked by sequencing and then subcloned into the Kpn1-Hind3 sites of pCB6 with a modified polylinker (De Silvestris et al. 1995 ).
Figure 1. The COOH-terminal polar peptide of b(5) is inaccessible to Ab if the ER membrane is not permeabilized. MDCK cells overexpressing wt b(5) were permeabilized with SLO (5 U/ml; see Materials and Methods), then fixed and processed for immunofluorescence in the presence (C, D, G, and H) or absence (A, B, E, and F) of Triton X-100. Cells were doubly labeled with the following pairs of Abs: polyclonal Ab raised against the 10 COOH-terminal amino acids of b(5) (A and C) and antitubulin mAb (B and D); polyclonal Ab against the catalytic domain of b(5) (E and G) and anti-PDI mAb (F and H). Polyclonal and monoclonal Abs were viewed with TRITC- and FITC-conjugated secondary Abs, respectively. The panels on the left and right side of the figure represent the same fields viewed under the rhodamine or fluorescein filters. Fields of cells treated or not treated with Triton X-100 were photographed and printed with the same exposures. Bar, 10 μm.
Figure 2. In vitro translated N-glyc b(5) becomes glycosylated in the presence of dog pancreas microsomes added either during or after translation. (A) COOH-terminal sequences of wt b(5) and of the N-glyc and O-glyc constructs. In all constructs, the hatched rectangle represents the COOH-terminal part of the membrane-anchoring domain. The underlined sequence in N-glyc b(5) corresponds to the first 19 amino acids of bovine opsin, and is connected to the COOH terminus of b(5) through a Ser and an Arg residue (italics). An N-glycosylation consensus sequence is boxed. The underlined sequence of O-glyc b(5), connected to the COOH terminus of b(5) via the SR sequence (italics), corresponds to residues 36–48 and residue 50 of mature human glycophorin A. The residues in boldface (Y between V48 and T50 and the three COOH-terminal prolines) were included to create an optimal consensus for O-glycosylation (Yoshida et al. 1997 ). The boxed residues are those that are glycosylated in native glycophorin A (Tomita and Marchesi 1975 ). (B) N-glyc b(5) (upper panel) or bean phaseolin (lower panel) synthetic RNAs were translated for 1 h in the rabbit reticulocyte system in the presence (lanes 1 and 2; Mbs co) or absence (lanes 3–6) of dog pancreas microsomes. One sample, which was first incubated in the absence of microsomes, was then treated with CHX, subjected to ultracentrifugation to remove ribosomes (see Materials and Methods), and further incubated for 1 h with microsomes (lanes 5 and 6; Mbs post). At the end of the incubations, samples were divided into two, denatured with SDS, and then incubated overnight in the presence (lanes 2, 4, and 6) or absence (lanes 1, 3, and 5) of Endo H (see Materials and Methods). The arrow in the upper panel indicates the Endo H–sensitive polypeptide (glycosylated N-glyc b) generated when microsomes were present during or after translation. The single and double asterisks in the lower panel indicate the mono- and diglycosylated forms of phaseolin, respectively (Ceriotti et al. 1991 ), which were generated only when membranes were present during the translation. Numbers on the left indicate the position and size (in kD) of Mr markers.
Cell Culture and Transfection
Most of the experiments in this study were conducted on transiently transfected CV1 cells that were cultured and transfected with the Ca2+PO4 method as described previously (De Silvestris et al. 1995 ). The efficiency of transfection was usually monitored by cotransfecting with green fluorescent protein (Clontech). For the fractionation experiment (see Fig 10), transfection was carried out with lipofectamine (GIBCO BRL) with 0.03 μg of b(5) cDNA/cm2 of culture dish surface. Cells were used for immunofluorescence or biochemical experiments within 24 h after transfection. In one experiment (see Fig 1), an MDCK line stably expressing wt b(5) was used. MDCK cells were cultured and transfected as described previously (Borgese et al. 1996 ). Several b(5)-expressing clones were obtained; however, the expression was completely lost after only a few passages in culture, so that further experiments with these clones could not be carried out.
Figure 3. Comparison of the distribution of overexpressed wt b(5) with that of endogenous ERGIC 53 in transfected CV1 cells incubated at 37 or 15°C. Transfected cells were incubated in DME, Hepes modification (Sigma Chemical Co.) in thermostated water baths for 5 h at 37°C (A–C) or 15°C (D–F), fixed and permeabilized, and doubly stained with anti-b(5) mAbs followed by TRITC-conjugated anti–mouse IgG (A and D), and polyclonal anti–ERGIC 53 followed by FITC-conjugated anti–rabbit IgG (B and E). A single confocal section is shown for each incubation condition. Images of the same field were acquired separately with Texas red (A and D) and fluorescein (B and E) filters. C and F show the merged images of the two acquisitions. Bar, 10 μm.
Figure 4. Velocity gradient analysis of b(5) solubilized from rat liver microsomes or transfected CV1 cells. Rat liver microsomes (A) or CV1 cells transfected with wt b(5) cDNA were lysed and loaded onto a 5–20% sucrose gradient containing 0.2% Triton X-100 and low salt, as described in Materials and Methods. Fractions were analyzed by Western blotting. Ribophorin (R) forms aggregates which distribute throughout the gradient and sediment into the pellet, whereas b(5) is found only in the top fractions, cosedimenting with cytochrome c. The vertical large and small arrowheads in both panels indicate the positions reached by cytochrome c (Mr ~12,300) and catalase (Mr ~232,000), respectively. Numbers on the left of the panels indicate the position and size (in kD) of Mr markers used in the Western blot analysis.
Figure 5. N-glyc and O-glyc b(5) have a reticular distribution in transfected cells and their catalytic domain is accessible to Abs restricted to the cytosol. CV1 cells transfected with N-glyc b(5) (A and B) or O-glyc b(5) (C and D) cDNA were permeabilized with SLO (30 μg/ml), and then fixed and doubly stained with mAbs against the catalytic domain of b(5) followed by TRITC-conjugated anti–mouse IgG (A and C), and with polyclonal Abs against the cytosolic tail of ERGIC 53 followed by FITC-conjugated anti–rabbit IgG (B and D). The figure shows single confocal sections of one field for each construct. The panels on the left and right side of the figure represent the same fields acquired with the Texas red or fluorescein filters. Asterisks indicate the nuclei of transfected cells. Note the clear staining of the nuclear envelope by anti-b(5) Abs both in N-glyc and O-glyc b(5)–transfected cells, indicative of ER localization. Bar, 10 μm.
Figure 6. The N-linked oligosaccharide of N-glyc b(5) retains Endo H sensitivity and Endo D resistance. (A) CV1 cells transfected with N-glyc b(5) cDNA were labeled for 2 h with Met/Cys, then chased for a further 6 h. One set of cells was exposed to BFA (10 μg/ml) 30 min before starting the labeling, and was kept with the drug for the entire pulse and chase period (lanes 5 and 6). At the end of the pulse (lanes 1 and 2) or after the chase (lanes 2–6), cells were harvested, lysed, and subjected to immunoprecipitation with antiopsin mAbs. Aliquots containing the same amounts of incorporated radioactive amino acid were used for each immunoprecipitation. One half of each immunoprecipitate was treated with Endo H (lanes 2, 4, and 6), whereas the other half was left untreated (lanes 1, 3, and 5). (B) CHO 15B cells, transfected with N-glyc b(5) cDNA, were labeled for 2 h and chased for 6 h with Met/Cys. One set of cells (lanes 3 and 4) was exposed to BFA as in A. At the end of the chase period, cells were harvested, lysed, and subjected to immunoprecipitation as in A. One half of the immunoprecipitates was treated with Endo D (lanes 2 and 4), whereas the other half was left untreated (lanes 1 and 3). The figure shows the result of the SDS-PAGE fluorography analysis of the Endo H– or Endo D–treated and untreated immunoprecipitates. The position of the 21-kD molecular mass marker is shown at the left of each panel. The vertical arrow in lane 2 of B indicates the position of the unglycosylated N-glyc b(5).
Figure 7. O-glyc b(5) becomes glycosylated in vivo. (A) Comparison of SDS-PAGE mobility of in vivo and in vitro synthesized O-glyc b(5). CV1 cells transfected with O-glyc b(5) cDNA were labeled for 2 h with Met/Cys, harvested, and subjected to immunoprecipitation with anti-b(5) Abs (lane 1). Alternatively, synthetic RNA coding for O-glyc b(5) was translated in vitro either in the absence (lane 2) or in the presence (lane 3) of dog pancreas microsomes. SDS-PAGE followed by fluorography fails to reveal a difference between the apparent Mr of the protein synthesized in vivo and that of the primary translation product produced in vitro. (B) Metabolic labeling of O-glyc b(5) with 3H-labeled sugars. CV1 cells, transfected with wt b(5) (lanes 1 and 2) or with O-glyc b(5) (lanes 3–6) cDNA, were incubated for 7 h with GlcNH2 (lanes 1–4) or Gal (lanes 5 and 6). For each labeling condition, one set of cells (lanes 2, 4, and 6) received 10 μg/ml of BFA 30 min before exposure to the labeled sugar, and the drug was maintained in the medium during the entire subsequent incubation. At the end of the incubation, cells were harvested, lysed, and aliquots containing the same amounts of incorporated radioactive sugar were subjected to immunoprecipitation with anti-b(5) Abs. Immunoprecipitates were analyzed by SDS-PAGE fluorography (upper panel). One fourth of the amounts used for immunoprecipitation were analyzed by Western blotting with anti-b(5) Abs (lower panel). The line on the left side of all panels indicates the position of the 21-kD molecular mass marker.
Figure 8. Time course of posttranslational addition of 3H-labeled sugar to O-glyc b(5). (A) Metabolic labeling with GlcNH2. Cells transfected with O-glyc b(5) were incubated for 3 h with GlcNH2 to allow for equilibration between UDP-GlcNAc and UDP-GalNAc. Cells from one dish were harvested at this point (lane 1), whereas the others were incubated for a further 1 (lanes 2 and 3) or 4 (lanes 4 and 5) h in the presence or absence of 15 μg/ml CHX as indicated. For each time point, cell lysates were prepared, and equal amounts of protein were used for immunoprecipitation with anti-b(5) Abs (upper panel). A proportional amount of each lysate (one fifth of the amount used for immunoprecipitation) was analyzed by Western blotting (lower panel). (B) Block of O-glyc b(5) synthesis by CHX. Cells transfected with O-glyc b(5) were incubated in parallel with those in A, but without added GlcNH2. After 3 h, Met/Cys was added and incubation was continued in the presence or absence of 15 μg/ml CHX, as indicated. At the indicated times, cell lysates were prepared and equal amounts of protein were used for immunoprecipitation, as in A. (C) Graphical representation of the results of A compared with the incorporation of 3H-labeled sugar into total protein. The graph on the right shows the ratios of band intensities of fluorographs (metabolically labeled O-glyc b) to those of the Western blots (total O-glyc b). Shown are the means from three sets of dishes ± SEM. The value for the ratio at 3 h (time of addition of CHX) has been normalized to 1. The graph on the left represents total TCA-precipitable 3H-labeled sugar normalized to total protein content. Squares, no CHX; triangles, CHX.
Figure 9. OKA inhibits sugar acquisition by O-glyc b(5). (A) CV1 cells transfected with O-glyc b(5) were incubated with GlcNH2 for 3 h to allow for equilibration between UDP-GlcNAc and UDP-GalNAc. At this time, one set of cells was harvested (lane 1), whereas the others were incubated for a further hour in the presence (lanes 4 and 5) or absence (lanes 2 and 3) of 1 μM OKA with or without 10 μg/ml BFA, as indicated. After clearing of lysates, equal amounts of protein were subjected to immunoprecipitation with anti-b(5) Abs (upper panel). A proportional amount of each lysate (one fifth of the amount used for immunoprecipitation) was analyzed by Western blotting (lower panel). (B) Graphical representation of the results of two experiments like the one in A. Two separate sets of dishes were labeled as described for A. The ratio of the intensities of the O-glyc b(5) bands detected by fluorography to that of the bands in corresponding samples detected by Western blotting is plotted. Shown are the means values ± half-range. (C) Immunofluorescence analysis of cells treated or not treated with 1 μM OKA. After 1 h with (C, panels d–f) or without (C, panels a–c) OKA, cells were fixed. Separate coverslips were analyzed for b(5) (C, panels a and d), ERGIC 53 (C, panels b and e), and giantin (C, panels c and f). Note the redistribution of ERGIC 53 induced by OKA, whereas O-glyc b(5) and giantin appear unaffected by the drug. Bar, 20 μm.
Figure 10. Intracellular distribution of O-glyc b(5). (A) O-glyc b(5) remains in the ER after prolonged incubation with CHX. CV1 cells transfected with O-glyc b(5) were incubated under the same conditions as in the experiments of Fig 8 and Fig 9, but without the labeled precursor and in the presence of 20 μg/ml of CHX for 4 (A, panels a–c) or 8 (A, panels d–f) h. Fixed cells were doubly labeled with anti-b(5) and anti–ribophorin I Abs (A, panels a–c), or with anti-b(5) and antigiantin Abs (A, panels d–f). A single confocal section is shown for the 4- and 8-h incubation. Images of the same field were acquired separately with the Texas red (A, panels a and d) and the fluorescein (A, panels b and e) filters. The corresponding merged images are shown in A, panels c and f (O-glyc b in red, marker protein in green). Note the absence of colocalization of O-glyc b(5) with giantin and its similar distribution to ribophorin I. The arrowheads in A, panels a–c indicate structures in which O-glyc b(5) accumulates at long times after transfection, and which are also positive for ribophorin I. Bar: (panels a–c) 10 μm; (panels d–f) 20 μm. (B) Optiprep density gradient analysis of CV1 cells transfected with O-glyc b(5) and metabolically labeled with GlcNH2. Cells were metabolically labeled with GlcNH2 for 6 h, then returned to DME for 4 h, before collection, homogenization, and preparation of a PNS, which was loaded under an 8–22% Optiprep gradient (see Materials and Methods). After centrifugation, fractions were collected and analyzed for O-glyc b(5) by Western blotting (B, panel a), NADPH-cyt c reductase enzyme activity (B, panel b), 3H-labeled O-glyc b(5) by immunoprecipitation followed by SDS-PAGE fluorography (B, panel c), and GS28 by Western blotting (B, panel d). The thick line positioned at the right of each graph covers the fractions containing the load zone of the gradient.
For the experiment shown in Fig 6 B we used CHO-15B cells grown in a 5% CO2 incubator in MEM with Earle's salts -modification, supplemented with 7.5% FCS, 2 mM glutamine, and antibiotics. These cells were transfected with the lipofectin (GIBCO BRL), using 0.2 μg of plasmid/cm2 of culture dish surface.
Antibodies
The following antibodies (Abs) were produced in our laboratory: (a) affinity-purified polyclonal Abs against b(5) raised in rabbits in our laboratory (Borgese and Meldolesi 1976 ; De Silvestris et al. 1995 ); (b) an affinity-purified polyclonal Ab directed against the 10 COOH-terminal residues of b(5). 2.4 mg of the peptide (LMYRLYMADD) was conjugated to 3 mg of chicken ovalbumin with succinimidyl 4--cyclohexane-1-carboxylate (Pierce) and used to immunize a rabbit. In addition, the following Abs were generously donated by the indicated investigators: a monoclonal anti-b(5) mAb from Dr. S. Park (Industrial Health Research Institute, Inchon, Korea) (Park et al. 1992 ); an antipeptide polyclonal antiserum against the 10 COOH-terminal amino acids of ERGIC 53 (QQEAAAKKFF) from Dr. Stefano Bonatti (University of Naples, Naples, Italy); polyclonal Abs against ribophorin I from Dr. Giovanni Migliaccio (Istituto di Ricerche di Biologia Molecolare, Pomezia, Italy) (Nicchitta et al. 1991 ) and Dr. Gert Kreibich (New York University School of Medicine, New York, NY) (Yu et al. 1990 ); an anti–? tubulin mAb (DM1) from Dr. Mark Kirschner (Harvard Medical School, Boston, MA); a mAb against the NH2-terminal peptide of bovine opsin (R2-15) from Dr. Paul Hargrave (University of Florida, Gainesville, FL) (Adamus et al. 1991 ); an antigiantin polyclonal serum from Dr. M. Renz (Institute of Immunology and Molecular Genetics, Karlsruhe, Germany) (Seelig et al. 1994 ). Anti–protein disulfide isomerase (PDI) and anti-GS28 mAbs were from StressGen Biotechnologies.
Immunofluorescence
Paraformaldehyde-fixed cells were permeabilized with Triton X-100 and processed for immunofluorescence as described previously (De Silvestris et al. 1995 ). In some experiments, permeabilization of the plasma membrane was carried out with streptolysin O (SLO), obtained from Dr. S. Bhakdi (Johannes-Gutenberg Universit?t, Mainz, Germany) (Bhakdi et al. 1993 ). Cells grown on coverslips were incubated with a buffer containing 115 mM K+acetate, 25 mM Hepes-KOH, pH 7.0, 2.5 mM MgCl2, 0.2 mM CaCl2, 1 mM EGTA, 12 mM glucose, 5–30 U/ml SLO for 10 min at 4°C. After removal of excess SLO, incubation was continued in the same buffer lacking SLO at 37°C for 30 min. Cells were observed under a Zeiss Axioplan microscope equipped for epifluorescence or with a Bio-Rad MRC 1024 ES laser confocal microscope.
Velocity Sucrose Gradient Centrifugation
CV1 cells transfected with wt b(5) in a 10-cm petri dish were washed free of medium with PBS, detached with a rubber policeman, sedimented, and resuspended in 200 μl of PBS and lysed for 10 min at 0°C with an equal volume of 2% Triton X-100, 40 mM NaCl, 50 mM Tris-Cl, pH 7.4, and protease inhibitors (2 mM phenylmethylsulfonyl fluoride, 1 μg/ml leupeptin, 1.4 μg/ml pepstatin, 2 μg/ml chymostatin) for 10 min on ice. A cleared lysate was obtained after centrifugation at 700 g for 10 min. The cleared lysate or a fraction of rat liver microsomes (1.3 mg of protein) solubilized under the same conditions as the cultured cells was loaded on top of a 12-ml 5–20% linear sucrose gradient containing 20 mM NaCl, 25 mM Tris-Cl, pH 7.4, 0.2% Triton X-100, in tubes of the SW40 rotor (Beckman Instruments, Inc.), and centrifuged at 39,000 rpm at 4°C for 16 h. Colored markers for sedimentation rates (cytochrome c and catalase) were run on a separate gradient centrifuged in parallel. 15 fractions were collected from the top with an Auto Densiflow probe (Buchler Instruments) and subjected to precipitation with TCA in the presence of 80 μg of cytochrome c as carrier. The precipitated proteins were analyzed by SDS-PAGE followed by Western blotting.
In Vitro Transcription and Translation
N-glyc and O-glyc b(5) in pGEM4 and a cDNA coding for the plant protein phaseolin cloned in pSP64T were transcribed from the SP6 promoter, and the resulting synthetic mRNA was translated for 1 h at 32°C in 10 or 20 μl of rabbit reticulocyte lysate (Promega Corp.) as described previously (Ceriotti et al. 1991 ), in the presence or absence of 1 μl of dog pancreas microsomes (Promega Corp.). In some samples, microsomes were added posttranslationally. In this case, the translation, carried out in the absence of microsomes, was stopped by addition of cycloheximide (CHX) (30 μg/ml), and elimination of ribosomes by centrifugation at 55,000 rpm for 1 h at 4°C in the Beckman TLA 100.3 rotor. The ribosome-free supernatants were then incubated for a further hour at 32°C in the presence of microsomes.
Metabolic Labeling Experiments
Metabolic labeling was carried out on CV1 or CHO15B cells, plated on 10-cm petri dishes, and transfected with b(5) or tagged versions thereof the day before exposure to the radioactive precursor. Labeling with 0.1–0.2 mCi/ml Met/Cys (Promix; Amersham Pharmacia Biotech) was carried out as described previously (Borgese et al. 1996 ). For labeling with high specific activity glucosamine (GlcNH2) or galactose (NEN Life Science Products or American Radiolabeled Chemicals, Inc.), cells were incubated for 1.5 h in MEM with Earle's salts containing glucose at reduced concentration (0.1 g/l) and 3% dialyzed FCS, before addition of the concentrated radioactive sugar to a final concentration of 0.3–0.6 mCi/ml. The length of the incubations, and the concentrations of added drugs (brefeldin A , okadaic acid , CHX; Sigma Chemical Co.) are specified in the figure legends.
Immunoprecipitation
Metabolically labeled cells were collected in PBS, lysed for 10 min at 0°C with an equal volume of 200 mM NaCl, 50 mM Tris-Cl, pH 7.4, 20 mM EDTA, 4% Triton X-100, and protease inhibitors. After clearing by centrifugation (1,000 g for 10 min), the lysates were analyzed for incorporation of the radioactive precursor and protein content. Aliquots of the lysates, containing equal amounts of incorporated radioactivity or equal amounts of protein, were precleared by incubation with protein A– or protein G–Sephrose beads in the presence of 0.2% gelatin, then incubated with anti-b(5) polyclonal Abs or antiopsin mAbs. The immune complexes were harvested with protein A– or protein G–Sepharose beads, in some cases treated with endoglycosidases, and finally analyzed by SDS-PAGE fluorography.
Cell Fractionation
Cell fractionation was carried out on cells plated on eight 10-cm petri dishes transfected with O-glyc b(5) and metabolically labeled with GlcNH2. All operations were carried out at 4°C. Cells were washed free of medium and detached with a rubber policeman. After collection by centrifugation, they were washed with homogenization solution (0.25 M sucrose, 0.5 mM EDTA, 0.5 mM EGTA, 20 mM Tris-Cl, pH 7.5, and protease inhibitors), resuspended in 1 ml of the same solution, and ruptured by eight passages through a cell cracker with a 0.0009-inch clearance. After elimination of nuclei by centrifugation (700 g for 10 min), the postnuclear supernatant (PNS) was brought to 27% wt/vol Optiprep (Nycomed), 20 mM tricine/NaOH, pH 7.8, 1.3% sucrose, and 1 mM EDTA, and layered under a linear 9.5-ml 8–22% isosmotic Optiprep gradient with the same ions as above. The gradients were topped with 0.3 ml of 8% sucrose plus ions, and centrifuged for 2 h at 28,000 rpm at 4°C in a Beckman SW41 rotor. Fractions were collected and equal aliquots were subjected to immunoprecipitation followed by SDS-PAGE fluorography or to Western blot analysis.
Biochemical Assays
Most of the techniques used in this study (SDS-PAGE, Western blotting, NADPH–cytochrome c enzyme assay) are described in previous publications (Borgese and Pietrini 1986 ; Borgese et al. 1996 ). Autoradiograms and fluorograms were scanned and band intensities determined using the NIH Image software.
For endoglycosidase (Endo) H treatment, immune complexes were detached from protein G–Sepharose beads by incubation for 3 min at 100°C in an equal volume of 40 mM Tris-Cl, pH 6.8, 4% SDS, 2% ?-mercaptoethanol, and 17% glycerol. After sedimentation of the beads, the supernatant was supplemented with five volumes of 0.1 M Na+ citrate buffer, pH 5.5, 0.6 μl of a 100-mg/ml solution of BSA and protease inhibitors, and then incubated overnight at 37°C with or without 10 mU of Endo H (Boehringer Mannheim). 5–10 μl of in vitro translation mix was similarly denatured and digested. For Endo D treatment, samples were denatured as for Endo H digestions, but the SDS-containing supernatants were diluted with five volumes of 0.25 M Na+phosphate, pH 7.2, 10 mM EDTA plus BSA, and protease inhibitors. Digestion was carried out overnight with 3 mU of Endo D (Boehringer Mannheim).
Results
Transmembrane Topology of b(5)
To plan a strategy for the investigation of the mechanism of residence of b(5) in the ER, it was first necessary to define the topology of the hydrophobic membrane-anchoring domain. Although b(5) is perhaps the first TA protein to have been characterized, there has been controversy as to whether it adopts a transmembrane disposition or whether it loops back into the cytosol. We investigated this problem with two different approaches as described below.
In the first approach, we used an Ab raised against the COOH terminus of b(5) (see Materials and Methods) to probe the accessibility of the COOH-terminal polar peptide by immunofluorescence in an MDCK cell line stably expressing b(5). Although this cell line originated from a single clone, only ~30% of the cells expressed detectable levels of b(5) at any one time. Cells were treated either with SLO to selectively permeabilize the plasma membrane (Bhakdi et al. 1993 ), or with Triton X-100 after fixation to permeabilize intracellular membranes. As shown in Fig 1, when the cells were permeabilized only with SLO, the cytosol became accessible to IgG, as demonstrated by the staining with antitubulin mAbs, which were equally effective with or without Triton X-100 permeabilization (compare Fig 1B and Fig D). In contrast, the ER lumen of SLO-permeabilized cells was poorly accessible, as demonstrated by the low (probably nonspecific) staining obtained with mAbs against the lumenal protein PDI (compare Fig 1F and Fig H). Under this same condition, the COOH terminus of b(5) was not accessible to Abs (Fig 1 A), which were, however, capable of binding their epitope after Triton X-100 treatment (Fig 1 C). In contrast to the anti–COOH-terminal peptide Ab, Abs raised against the catalytic domain of b(5) were able to bind the antigen regardless of the permeabilization protocol (Fig 1E and Fig G). The results illustrated in Fig 1 are evaluated quantitatively in Table 1, and are consistent with a lumenal location of the COOH-terminal polar peptide of b(5).
Table 1. Quantitative Analysis of b(5) Immunofluorescence in Transfected MDCK Cells Permeabilized with SLO or with SLO + Triton X-100
In the second approach, the COOH terminus of b(5) was extended with a sequence containing a consensus for N-glycosylation, as reporter for translocation into the ER lumen. The appended sequence (Fig 2 A) was derived from the NH2 terminus of bovine opsin. The resulting construct, N-glyc b(5), was translated in vitro under different conditions. As shown in the upper panel of Fig 2 B, lane 1, when N-glyc b(5) was translated in the presence of dog pancreas microsomes, two bands were obtained, of which one comigrated with the product obtained in the absence of membranes (lanes 3 and 4), and the other, indicated by the arrow, had a slower mobility and was Endo H–sensitive (lane 2), demonstrating that N-glyc b(5)'s COOH terminus is translocated across the membrane to become glycosylated. More importantly, if N-glyc b(5) was first translated, and microsomes that were added after translation were blocked by CHX, and ribosomes were removed by sedimentation, N-glyc b(5) was still glycosylated with high efficiency (lanes 5 and 6), demonstrating that the hydrophobic domain is capable of translocating downstream residues posttranslationally. As a control, we analyzed the behavior of phaseolin, a plant vacuolar glycoprotein that is translocated across the ER cotranslationally (Ceriotti et al. 1991 ). As shown in the lower panel of Fig 2 B, lane 1, phaseolin was modified to the mono- and diglycosylated forms (marked by one and two asterisks, respectively) when microsomes were present during translation, but remained unglycosylated when membranes were added after translation (lanes 5 and 6).
b(5) Overexpressed in CV1 Cells Is in the ER in a Nonaggregated State
In mammalian cells, the first station after exit from the ER is a tubular vesicular compartment, also known as an intermediate compartment (IC) (Bannykh and Balch 1997 ). Some proteins that are kept in the ER by a retrieval mechanism can be detected by immunofluorescence in the IC (Jackson et al. 1993 ; Martire et al. 1996 ; Lotti et al. 1999 ), and this IC localization can be increased by incubation at 15°C, a temperature that blocks exit from the IC (Jackson et al. 1993 ). We investigated whether this was also the case for b(5) by comparing its intracellular distribution with that of ERGIC 53, a marker for the IC (Schweizer et al. 1988 ), after incubation of transfected CV1 cells at 37 or 15°C. As can be seen in Fig 3b(5) could not be detected in structures enriched in ERGIC 53 either under normal incubation conditions (Fig 3, A–C), or after prolonged incubation at 15°C (Fig 3, D–F). Under the latter condition, ERGIC 53–containing elements clustered in the Golgi area (compare Fig 3E and Fig B) in agreement with the recent observations of Klumperman et al. 1998 . It should be mentioned that at longer times after transfection (>24 h), b(5) was often seen to concentrate in large structures that were positive for ER markers (see Fig 10). These structures may be related to the karmellae, which are induced in yeast cells by overexpression of b(5) (Vergeres et al. 1993 ). To avoid excessive formation of these structures, all the experiments described in this paper were initiated within 24 h after transfection.
Because a number of ER membrane proteins, including the ribophorins, are found in rapidly sedimenting aggregates after solubilization of microsomes with nonionic detergents, it is thought that in situ they form an intramembranous proteinaceous network, which could also be the basis for their retention in the ER (Yu et al. 1989 ). To investigate whether overexpressed b(5) might belong to such an aggregate, we analyzed its sedimentation on sucrose velocity gradients after detergent extraction from transfected CV1 cells and compared it with that of ribophorin I and of b(5) endogenous to rat liver microsomes. As can be seen from Fig 4, under the conditions used, ribophorin I extracted both from rat liver microsomes (Fig 4 A) and from transfected CV1 cells (Fig 4 B) formed rapidly sedimenting aggregates, in agreement with published work (Hortsch et al. 1986 ; Yu et al. 1989 ). In contrast, b(5) from rat liver microsomes or transfected CV1 cells was recovered in the upper fractions of the gradient, cosedimenting with cytochrome c as expected for the monomeric form of the protein (Mr ~15,000), suggesting that it exists in a freely diffusible form within the ER of the transfected cells.
Use of Tagged Versions of b(5) to Follow Its Intracellular Trafficking
To investigate with biochemical methodology whether b(5) is retrieved from a downstream compartment, we used COOH-terminally appended tags to report on the intracellular compartments visited by b(5) during its lifetime. In addition to N-glyc b(5) described above, we constructed a mutant with potential O-glycosylation sites at the COOH terminus (O-glyc b; Fig 2 A). The sequence chosen was derived from human glycophorin A (residues 35–48), followed by the sequence YTPPP, in which the Thr residue is in an optimal consensus for O-glycosylation (Yoshida et al. 1997 ).
We first checked by immunofluorescence whether the added tags altered the intracellular distribution of b(5) in transiently transfected CV1 cells. As shown in Fig 5, both polypeptides had a reticular distribution and a clear localization to the nuclear envelope, indicative of an ER localization. Moreover, like the wt protein, they were not concentrated in structures enriched in ERGIC 53, and their catalytic domain was accessible to Abs restricted to the cytosol, as demonstrated by the good reaction obtained in cells permeabilized only with SLO.
The Majority of N-glyc b(5) Does Not Reach the Compartment of Residence of Golgi Mannosidases I and II
To see whether the N-glycan of N-glyc b(5) is modified by mannosidase II, which is generally localized in the medial Golgi cisterna (Velasco et al. 1993 ), we investigated whether the metabolically labeled protein could acquire Endo H resistance. Cells were labeled with Met/Cys for 2 h, then chased for 6 h, and N-glyc b(5) was immunoprecipitated and analyzed by SDS-PAGE fluorography. As shown in Fig 6 A, lanes 1 and 2, after the 2 h pulse, most of the in vivo synthesized N-glyc b(5) was glycosylated and Endo H–sensitive; Endo H sensitivity was completely retained also after 6 h of chase (Fig 6 A, lanes 3 and 4). Since some N-linked glycans are not accessible to mannosidase II, even if they do transit through the Golgi, we checked whether the high mannose oligosaccharide attached to N-glyc b(5) could be modified by mannosidase II if forced into a common intracellular compartment. When cells were incubated with BFA to relocate Golgi enzymes to the ER (Lippincott-Schwartz et al. 1989 ), a portion of N-glyc b(5) was converted to a more slowly migrating Endo H–resistant polypeptide (Fig 6 A, lanes 5 and 6). We conclude that under normal conditions N-glyc b(5) does not reach the compartment of residence of mannosidase II.
An earlier step in N-glycan processing is trimming by mannosidase I, an event that can be monitored by assessing the acquisition of sensitivity to Endo D. We investigated the Endo D sensitivity of N-glyc b(5) in CHO 15B cells, which lack N-acetylglucosamine (GlcNac) transferase I activity, to avoid a possible loss of Endo D sensitivity by further processing in the Golgi. As shown in Fig 6 B, nearly all of the N-glyc b(5) remained Endo D–resistant after 6 h of chase (Fig 6 B, lanes 1 and 2). However, compared with the nondigested sample, a small increase in the amount of deglycoyslated polypeptide was visible after Endo D treatment (Fig 6 B, arrow), suggesting that a small proportion of the tagged b(5) may have had access to mannosidase I. After incubation with BFA, all of the N-glyc b(5) became Endo D–sensitive (Fig 6 B, lanes 3 and 4). These results indicate that the vast majority of N-glyc b(5) molecules do not reach the compartment of residence of mannosidase I during a 6-h chase.
Glycosylation of O-glyc b(5)
The results presented in Fig 6 indicate that N-glyc b(5) does not recycle through the medial Golgi; however, it was possible that it reaches an earlier Golgi subcompartment. To investigate this possibility, we turned to the O-glyc b(5) construct. The first step in O-glycosylation is attachment of an N-acetylgalactosamine (GalNac) residue to Thr or Ser residues, and the enzymes responsible for this reaction, the GalNac transferases, have been localized to the cis-Golgi as well as to more distal cisternae (Rottger et al. 1998 ).
We first compared the electrophoretic mobility of in vivo synthesized O-glyc b(5) with that of the in vitro generated primary translation product. As shown in Fig 7 A, the product expressed in transfected cells (Fig 7 A, lane 1) comigrated with the product synthesized in vitro in the absence (Fig 7 A, lane 2) or presence (Fig 7 A, lane 3) of membranes. However, if cells were incubated with BFA, O-glyc b(5) was shifted to a higher apparent Mr (compare Fig 7 B, lanes 3 and 4, or Fig 7 B, lanes 5 and 6), indicating that at least one of the potential O-glycosylation sites could be used if the protein came into contact with the relevant enzymes. To see whether in the absence of BFA the initial steps of O-glycosylation were also taking place but were not resulting in reduced electrophoretic mobility of O-glyc b(5), we carried out metabolic labeling experiments with 3H-labeled sugars. As shown in Fig 7 B, incubation with GlcNH2, which serves as precursor both to UDP-GlcNac and to UDP-GalNac, resulted in labeling of O-glyc b(5) both in the absence (Fig 7 B, lane 3) and the presence (Fig 7 B, lane 4) of BFA. The labeling was specific, because under the same conditions, wt b(5) was not labeled (Fig 7 B, lanes 1 and 2), although it was efficiently expressed, as shown by the Western blot in the lower part of Fig 7 B.
The second sugar to be added on O-linked oligosaccharides is galactose. With galactose as radioactive precursor, O-glyc b(5) became labeled in the presence of BFA (Fig 7 B, lane 6), and a weak signal was obtained also in the absence of the drug (Fig 7 B, lane 5). Thus, at steady-state, a small portion of the O-glyc mutant has also undergone the second step of O-glycosylation.
To investigate how rapidly glycosylation of O-glyc b(5) occurs after its synthesis, we followed the time course of incorporation of 3H-labeled sugar after blocking protein synthesis with CHX (Fig 8). Cells were first incubated for 3 h with GlcNH2 to allow for equilibration between UDP-GlcNac and UDP-GalNac. Incubation was then continued in the presence or absence of CHX. To control for the efficacy of the block in protein synthesis, a separate set of dishes of transfected cells was incubated in parallel with Met/Cys in the presence or absence of CHX, and O-glyc b(5) immunoprecipitates were then analyzed (Fig 8 B). CHX efficiently blocked the synthesis of O-glyc b(5) (Fig 8 B; compare lanes 2 and 4 with lanes 1 and 3). However, as shown in Fig 8 A and on the graph on the right side of Fig 8 C (obtained by normalizing the amount of immunoprecipitated 3H-labeled O-glyc b to the amount of O-glyc b expressed, as determined by Western blotting), the block in protein synthesis had no effect at all on the rate of sugar incorporation, which continued at a linear rate for 4 h after addition of the drug. This result stands in sharp contrast to the strong inhibitory effect of CHX on the incorporation of labeled sugar into total cellular proteins (graph on the left side of Fig 8 C). Thus, there is a large pool of unglycosylated O-glyc b(5) molecules that acquire O-linked sugar at a low rate. It should be mentioned that incubation with CHX for 4 h did not cause an appreciable decrease in the total amount of O-glyc b(5) or in the accumulation of the labeled species (compare Fig 8 A, lanes 4 and 5) in this and other experiments, indicating that under these conditions O-glyc b(5) is stable. The variations in the amounts sometimes detected in Western blots (e.g., Fig 8 A, lanes 3–5 vs. Fig 8 A, lanes 1 and 2) are presumably due to differences in transfection efficiencies in the different dishes.
The bulk of the available evidence indicates that the process of O-glycosylation occurs in the Golgi complex (Roth et al. 1994 ; Schweizer et al. 1994 ; Rottger et al. 1998 ). However, under some conditions, especially in infected cells, the initial steps may take place in a compartment upstream of the Golgi (discussed in Rottger et al. 1998 ). Moreover, recent evidence indicates that Golgi-resident enzymes slowly recycle through the ER (Cole et al. 1998 ; Storrie et al. 1998 ; Girod et al. 1999 ). To investigate whether O-glyc b(5) must leave the ER to become glycosylated, we treated cells with the phosphatase inhibitor OKA, a drug which blocks exit from the ER (Davidson et al. 1992 ; Pryde et al. 1998 ). Transfected cells were exposed to GlcNH2 for 3 h and then incubated further for another hour in the presence or absence of OKA. At this time cells were collected for biochemical analysis or analyzed by immunofluorescence. As shown in Fig 9 C, the intracellular localization of O-glyc b(5) (Fig 9 C, panels a and d) and of a Golgi marker (giantin; Fig 9 C, panels c and f) were unaffected by OKA. In contrast, ERGIC 53 was dispersed from the Golgi area to more peripherally located structures (compare Fig 9 C, panels e and b). These results are consistent with OKA's inhibition of ER-to-Golgi transport. At slightly later times of incubation, ERGIC 53 appeared uniformly distributed within the ER, but the cells began to suffer and to retract from the substrate (data not shown). Analysis by immunoprecipitation and Western blotting (Fig 9A and Fig B) showed a 3.2-fold increase in labeling of O-glyc b(5) between 3 and 4 h in the absence of OKA, and an ~50% inhibition of this increase by OKA. This is a fairly strong effect if one considers that OKA does not exert its full inhibitory activity immediately after addition (Davidson et al. 1992 ).
To exclude the possibility that OKA was decreasing O-glyc b(5) glycosylation through a direct or indirect inhibition of glycosyl transferases and not by a transport block, we analyzed its effect in the presence of BFA. As can be seen in Fig 9 A, the effect of OKA was reversed in the presence of BFA (Western blot; Fig 9 A, lanes 3 and 5). During a 1-h period of incubation with BFA, 41.7 ± 1.7% and 37.6 ± 1.6% (average ± half-range of two experiments) of O-glyc b(5) was converted to the slower migrating, fully processed form in the absence and presence of OKA, respectively.
Another important piece of information in Fig 9 can be obtained by examining the ratio of specific radioactivity (immunoprecipitate/Western) of O-glyc b(5) attained in the absence and presence of BFA (Fig 9 A, lanes 2 and 3). By scanning a lower exposure of fluorographs in which the bands labeled in the presence of BFA had not saturated the film (data not shown), we found that the specific radioactivity attained in 1 h by O-glyc b(5) in the absence of drugs was ~7% that attained by the lower Mr polypeptide of the doublet generated in the presence of BFA. Since the higher Mr band presumably contains additional labeled sugar, it could not be compared with the more rapidly migrating polypeptide. If one assumes that the lower Mr band of Fig 9 A, lane 3 is 100% glycosylated, this would indicate a half-time for glycosylation of O-glyc b(5) (in the absence of BFA) of ~10 h, in agreement with the slow acquisition of sugar after the blockade of protein synthesis demonstrated in Fig 8. This half-time may be an underestimate, since a fraction of the low Mr polypeptide molecules of Fig 9 A, lane 3 may be unglycosylated.
The results of Fig 9 suggest that O-glyc b(5) must leave the ER to become glycosylated. But does O-glyc b(5) return to its compartment of origin once it has exited? This question was investigated both by immunofluorescence and by cell fractionation (Fig 10). We carried out immunofluorescence analysis of transfected cells after long exposures (4 and 8 h) to CHX. From the data of Fig 8O-glyc b(5) acquires sugar linearly for up to 4 h in the presence of CHX, and on the basis of the estimate of 10 h for the half-time of O-glycosylation (Fig 9), ~25% of O-glyc b(5) molecules should have acquired sugar at this time. A concentration of these glycosylated molecules in the glycosylation compartment (cis-Golgi) should have been detectable by immunofluorescence. However, as shown in Fig 10 A, the tagged protein retained a similar distribution to that of the ER protein ribophorin I at 4 h of incubation (Fig 10 A, panels a–c), and did not colocalize with the Golgi marker giantin even after 8 h of incubation with CHX (Fig 10 A, panels d–f). Fig 10 A, panels a–c also show an example of the b(5)-rich structures that began to appear in some of the cells in this experiment (the arrowheads indicate two such structures). As shown in Fig 10 A, panels b and c, ribophorin I also localized to these structures, suggesting that they represent proliferations of the ER. The frequency of these structures was, in any case, the same in cells incubated with or without CHX (data not shown).
The subcellular localization of glycosylated O-glyc b(5) was also analyzed by Optiprep density gradient centrifugation of a PNS from cells metabolically labeled with GlcNH2 (Fig 10 B). Under the conditions used, the ER marker NADPH-cyt P450 reductase showed a sharp peak of activity centered at fraction 6, corresponding to a density of 1.1 (Fig 10 B, panel b), whereas GS28, a marker for the cis-Golgi (Subramaniam et al. 1995 ), was broadly distributed throughout the gradient and present also in the bottom fractions immediately adjacent to the load zone (Fig 10 B, panel d). Total O-glyc b(5), detected by Western blot (Fig 10 B, panel a), peaked at a slightly lower density (fraction 5) than the reductase. A portion of O-glyc b(5) floated to the top of the gradient. This material probably corresponds to membrane fragments of low density, which we have not characterized further. Finally, 3H-labeled O-glyc b(5), detected by immunoprecipitation (Fig 10 B, panel c), had a distribution similar to that of total O-glyc b(5), and was depleted from the region of the gradient more enriched in GS28 (fractions 7–9). These results suggest that unglycosylated and glycosylated O-glyc b(5) molecules coexist within the same compartment, and also that both may be enriched in smooth subdomains of the ER.
Discussion
Both retention and retrieval mechanisms are thought to be involved in keeping ER resident proteins from escaping down the secretory pathway. The identification of specific retrieval sequences has spurred a large amount of work that has resulted in a significant increase in our understanding of the retrograde pathway (Pelham and Munro 1993 ; Cosson and Letourneur 1994 ; Teasdale and Jackson 1996 ; Cosson et al. 1998 ). However, most of this work has been carried out on chimeras, consisting of a retrieval signal grafted onto a protein normally destined for export from the ER, and there is still not much information on the relative roles of retention and retrieval in determining the residence of bona fide ER proteins. A few mammalian ER membrane proteins have been studied by analyzing the processing of N-linked glycans attached to endogenous or engineered consensus sites. Due the failure of these proteins to acquire Endo H resistance, it has been concluded that they reside in the ER by a true retention mechanism (Ahn et al. 1993 ; Masaki et al. 1996 ; Duvet et al. 1998 ; Honsho et al. 1998 ). However, since Endo H resistance is acquired in the medial Golgi, these studies could not exclude that retrieval from an earlier Golgi compartment was occurring. In this study, we have addressed this problem by attaching short sequences, containing either N- or O-glycosylation sites, to the COOH terminus of b(5), a TA protein of the ER. We show that in the O-glyc mutant at least one glycosylation site is used, indicating that the tagged protein comes in contact with cis-Golgi enzymes, an event which could not be detected by analysis of the oligosaccharide of the N-glyc–tagged version. The methodology used here should also be useful for the study of the trafficking of other ER membrane proteins, particularly of those lacking lumenal domains with endogenous glycosylation sites.
Posttranslational Translocation of the COOH Terminus of b(5) across the ER Membrane
Before undertaking an investigation of the intracellular sorting of b(5), we judged it necessary to define the topology of its membrane-anchoring domain. Although this problem has been the object of numerous investigations, there were still conflicting views as to whether b(5)'s hydrophobic domain adopts a transmembrane disposition with the extreme COOH-terminal residues in the lumen of the ER, or whether it has a hairpin topology with the COOH terminus looping back into the cytosol (Dailey and Strittmatter 1981 ; Arinc et al. 1987 ; Ozols 1989 ; Chester et al. 1992 ; Borgese et al. 1993 ; Vergeres et al. 1995 ; Kuroda et al. 1996 ). However, strong evidence for a transmembrane topology for b(5) was provided recently by the finding that a tagged version bearing an N-glycosylation consensus sequence at the COOH terminus acquired N-linked carbohydrate (Honsho et al. 1998 ). Although this study proved that the COOH terminus of this construct is translocated into the ER lumen in vivo, it did not investigate the mechanism of this translocation, leaving open the possibility that the addition of polar residues at the COOH terminus could cause a translocation that does not occur with the wt, untagged polypeptide. For instance, the additional 15–20 COOH-terminal amino acids could lead to a partial exposure of residues of the hydrophobic domain before termination of translation, resulting in the binding of the signal recognition particle and in a translocon-dependent translocation. For this reason, and since the wt protein is synthesized on free polysomes and inserts into membranes after release from the ribosomes, it was important to establish that the translocation of the COOH terminus of COOH-terminally tagged b(5) could occur posttranslationally in the absence of ribosomes. Our results with the N-glyc b(5) mutant show that this is indeed the case, a strong indication that in the wt protein the seven polar COOH-terminal residues are also in the lumen of the ER. In agreement with this conclusion, in immunofluorescence experiments we found that the COOH-terminal polar peptide is not accessible to Abs unless the ER membrane is permeabilized with Triton X-100. Taken together these results justify the use of COOH-terminally tagged versions of b(5) to study its intracellular trafficking.
Although the hydrophobic domain of b(5), in its ability to translocate downstream residues across the ER membrane, superficially resembles the signal anchor sequences of classical type II proteins, the mechanism by which it functions is quite different, since it operates on the released polypeptide in the absence of ribosomes. An in vitro posttranslational translocation similar to that of the b(5) COOH terminus has been shown also for synaptobrevin I (Kutay et al. 1995 ), a synaptic vesicle soluble N-ethylmaleimide–sensitive factor attachment protein receptor with a considerably longer hydrophobic domain than b(5). The insertion of synaptobrevin appeared to require proteins different from those of the classical Sec61-based translocation apparatus. It is likely that b(5) and synaptobrevin, as well as all other TA proteins, translocate their COOH terminus with the same mechanism, which certainly deserves further investigation.
Retention or Retrieval?
To investigate whether b(5) is retrieved from the IC or from the cis-Golgi, we first compared its distribution by immunofluorescence with that of the IC marker, ERGIC 53, after incubation either under normal conditions or at 15°C, a temperature which interferes with trafficking between the ER and the Golgi, and which has been shown in some cases to cause accumulation of recycling ER proteins in the IC (Jackson et al. 1993 ). However, for b(5), this approach did not yield any evidence in favor of its movement out of the ER. Proteins that recycle slowly may not be captured in the IC by incubation at low temperature (Jackson et al. 1993 ), presumably because entry as well as exit from the IC may be slowed. Therefore, we turned to the use of lumenally tagged versions of b(5) (N-glyc and O-glyc b), with the aim of using the attached oligosaccharide chains as reporters for the intracellular compartments visited by b(5). These tagged constructs were inserted into membranes with the correct topology, and had an intracellular distribution indistinguishable from that of transiently expressed wt b(5). During a 6-h chase, N-glyc b(5) did not acquire Endo H resistance, and also remained nearly completely Endo D–resistant, suggesting that it was not reaching the medial Golgi. However, when we turned to a more stringent assay based on the incorporation of sugar into the O-glyc mutant, we found that at least one O-glycosylation site was used, indicating that the protein was coming into contact with a GalNac transferase, enzymes which are localized to the Golgi complex (Rottger et al. 1998 ). We believe that the acquisition of carbohydrate by O-glyc b(5) is reporting on a recycling event through the cis-Golgi, for the reasons detailed below.
Processing of a glycoprotein by Golgi enzymes has normally been taken as evidence for its passage though the Golgi complex. However, recent evidence showing that Golgi enzymes recycle slowly through the ER (Cole et al. 1998 ; Storrie et al. 1998 ; Girod et al. 1999 ) makes it more difficult to interpret the significance of Golgi modifications on ER proteins. Nonetheless, since ER proteins generally do not carry Golgi modifications, it seems that these recycling Golgi enzymes are not active within the ER. Therefore, it is probable that O-glyc b(5) acquired its sugar after leaving the ER, and this idea is supported by the finding that glycosylation of O-glyc b(5) could be inhibited by the phosphatase inhibitor OKA, which blocks transport out of the ER (Davidson et al. 1992 ; Pryde et al. 1998 ). If O-glyc b(5) had been modified within the ER by recycling Golgi enzymes, OKA might actually have increased the processing of O-glyc b(5) by the trapped glycosyl transferases. Another explanation for our data is that the tagged protein, after exiting the ER and becoming glycosylated, did not return to its compartment of origin. This interpretation is unlikely, since no redistribution of O-glyc b(5) from the ER to another compartment could be observed after a chase with CHX under conditions in which the proportion of glycosylated O-glyc b(5) molecules was increasing at a linear rate. Moreover, GlcNH2-labeled and total O-glyc b(5) had similar distributions on an Optiprep density gradient, suggesting that they coexist in the same intracellular compartment.
Does the behavior of overexpressed O-glyc b(5) reflect that of endogenous b(5) in mammalian cells? It is possible that overexpression causes leakage from the ER of the tagged b(5) or that the tag itself alters the behavior of b(5). Although we cannot exclude either of these possibilities, the important finding here is that b(5) appears to have the capacity to be captured and returned to the ER from a downstream compartment, even though the extent of exit from the ER for the endogenous molecule and the overexpressed tagged mutant may be different. The rate of acquisition of carbohydrate by O-glyc b(5) was in any case quite slow: by comparing the extent of labeling of the tagged protein in the presence or absence of BFA, we estimated a half-time for acquisition of O-linked GalNac of ~10 h. This slow rate of glycosylation, as well as the lack of colocalization of wt and tagged versions of b(5) with markers for the IC, suggest that b(5) tends to be excluded from budding transport vesicles, and that retrieval from a downstream compartment represents a salvage mechanism for those molecules that occasionally leak out of the ER. In other words, it would appear that both retention and retrieval are operating together to keep b(5) in the ER. We do not know at present whether retention is based simply on the lack of a positive export signal and/or the presence of a positive retention signal or feature in b(5). Formation of oligomeric complexes has been suggested to result in retention of some ER proteins (Yu et al. 1989 ). However, this mechanism would not seem to be responsible for b(5) retention. Indeed, our sucrose gradient analysis did not reveal the presence of b(5) oligomers under conditions in which high-Mr complexes containing ribophorin I were preserved. Consistent with this result, preliminary experiments carried out with the fluorescence recovery after photobleaching technique suggest that green fluorescent protein–b(5) chimeras diffuse rapidly across the ER (Snapp, E., and J. Lippincott-Schwartz, personal communication).
Our previous work demonstrated that a short hydrophobic domain is required to keep b(5) in the ER; lengthening of the TMD results in escape of b(5) from the ER and its arrival at the plasma membrane (Pedrazzini et al. 1996 ). The extension of this finding by other laboratories to other TA proteins and reporter constructs (Rayner and Pelham 1997 ; Yang et al. 1997 ; Honsho et al. 1998 ) suggests that TMD-dependent sorting may be a general phenomenon for TA proteins and may occur by a common mechanism. The results of the present study, which suggest that both retention and retrieval mechanisms are operating to keep b(5) in the ER, raise the question as to whether the short TMD is required for retention, retrieval, or for both these phenomena. If the TMD is involved in retrieval, a candidate recycling receptor involved in this process is rer1p, a protein demonstrated to be required for ER residence of a number of membrane polypeptides in yeast via recognition of their TMDs (Sato et al. 1996 , Sato et al. 1997 ). This receptor, which also has been cloned from mammalian cells (Fullekrug et al. 1997 ), appears to prefer short and somewhat hydrophilic TMDs (Letourneur and Cosson 1998 ). On the other hand, retrieval of TA proteins may occur by a completely different mechanism, since Ufe1p, a TA target soluble N-ethylmaleimide–sensitive factor attachment protein receptor of the ER, does not change its localization in rer1p-deficient yeast cells (Rayner and Pelham 1997 ). Further work with tagged versions of TA proteins like the ones described in this study should help to define at the molecular level the sorting mechanisms of this class of proteins.
References
Adamus, G., Arendt, A., Hargrave, P.A. 1991. Genetic control of antibody response to bovine rhodopsin in mice: epitope mapping of rhodopsin structure. J. Neuroimmunol. 34:89-97.
Ahn, K., Szczesna-Skorupa, E., Kemper, B. 1993. The amino-terminal 29 amino acids of cytochrome P450 2C1 are sufficient for retention in the endoplasmic reticulum. J. Biol. Chem. 268:18726-18733.
Arinc, E., Rzepecki, L.M., Strittmatter, P. 1987. Topography of the C-terminus of cytochrome b5 tightly bound to dimyristoylphosphatidylcholine vesicles. J. Biol. Chem. 262:15563-15567.
Bannykh, S.I., Balch, W.E. 1997. Membrane dynamics at the endoplasmic reticulum-Golgi interface. J. Cell Biol. 138:1-4.
Bhakdi, S., Weller, U., Walev, I., Martin, E., Jonas, D., Palmer, M. 1993. A guide to the use of pore-forming toxins for controlled permeabilization of cell membranes. Med. Microbiol. Immunol. 182:167-175.
Borgese, N., Meldolesi, J. 1976. Immunological similarity of the NADH-cytochrome c electron transport system in microsomes, Golgi complex and mitochondrial outer membrane of rat liver cells. FEBS Lett. 63:231-234.
Borgese, N., Pietrini, G. 1986. Distribution of the integral membrane protein NADH-cytochrome b5 reductase in rat liver cells, studied with a quantitative radioimmunoblotting assay. Biochem. J. 239:393-403.
Borgese, N., D'Arrigo, A., De Silvestris, M., Pietrini, G. 1993. NADH-cytochrome b5 reductase and cytochrome b5—the problem of posttranslational targeting to the endoplasmic reticulum. In Borgese N., Harris J.R., eds. Subcellular Biochemistry. Vol. 21. New York, Plenum Press, 313-341.
Borgese, N., Aggujaro, D., Carrera, P., Pietrini, G., Bassetti, M. 1996. A role for N-myristoylation in protein targeting: NADH-cytochrome b5 reductase requires myristic acid for association with outer mitochondrial but not endoplasmic reticulum membranes. J. Cell Biol. 135:1501-1513.
Brewer, C.B., Roth, M.G. 1991. A single amino acid change in the cytoplasmic domain alters the polarized delivery of influenza virus hemagglutinin. J. Cell Biol. 114:413-421.
Ceriotti, A., Pedrazzini, E., Fabbrini, M.S., Zoppè, M., Bollini, R., Vitale, A. 1991. Expression of the wild-type and mutated vacuolar storage protein phaseolin in Xenopus oocytes reveals relationships between assembly and intracellular transport. Eur. J. Biochem. 202:959-968.
Chester, D.W., Skita, V., Young, H.S., Mavromoustakos, T., Strittmatter, P. 1992. Bilayer structure and physical dynamics of the cytochrome b(5) dimyristoylphosphatidylcholine interaction. Biophys. J. 61:1224-1243.
Cole, N.B., Ellenberg, J., Song, J., DiEuliis, D., Lippincott-Schwartz, J. 1998. Retrograde transport of Golgi-localized proteins to the ER. J. Cell Biol. 140:1-15.
Cosson, P., Letourneur, F. 1994. Coatomer interaction with di-lysine endoplasmic reticulum retention motifs. Science. 263:1629-1631.
Cosson, P., Lefkir, Y., Démollière, C., Letourneur, F. 1998. New COP1-binding motifs involved in ER retrieval. EMBO (Eur. Mol. Biol. Organ.) J. 17:6863-6870.
Dailey, H.A., Strittmatter, P. 1981. Orientation of the carboxyl and NH2 termini of the membrane-binding segment of cytochrome b5 on the same side of phospholipid bilayers. J. Biol. Chem. 256:3951-3955.
Davidson, H.W., McGowan, C.H., Balch, W.E. 1992. Evidence for the regulation of exocytic transport by protein phosphorylation. J. Cell Biol. 116:1343-1355.
De Silvestris, M., D'Arrigo, A., Borgese, N. 1995. The targeting information of the mitochondrial outer membrane isoform of cytochrome b5 is contained within the carboxyl-terminal region. FEBS Lett. 370:69-74.
Duvet, S., Cocquerel, L., Pillez, A., Cacan, R., Verbert, A., Moradpour, D., Wychowski, C., Dubuisson, J. 1998. Hepatitis C virus glycoprotein complex localization in the endoplasmic reticulum involves a determinant for retention and not retrieval. J. Biol. Chem. 273:32088-32095.
Fullekrug, J., Boehm, J., Rottger, S., Nilsson, T., Mieskes, G., Schmitt, H.D. 1997. Human Rer1 is localized to the Golgi apparatus and complements the deletion of the homologous Rer1 protein of Saccharomyces cerevisiae. Eur. J. Cell Biol. 74:31-40.
Giordano, S.J., Steggles, A.W. 1992. Identification and nucleotide sequence of the leukocyte and reticulocyte forms of rabbit cytochrome b5 mRNA. SAAS Bull. Biochem. Biotechnol. 5:13-17.
Girod, A., Storrie, B., Simpson, J.C., Johannes, L., Goud, B., Roberts, L.M., Lord, J.M., Nilsson, T., Pepperkok, R. 1999. Evidence for a COP-I-independent transport route from the Golgi complex to the endoplasmic reticulum. Nat. Cell Biol. 1:423-430.
Honsho, M., Mitoma, J., Ito, A. 1998. Retention of cytochrome b(5) in the endoplasmic reticulum is transmembrane and luminal domain-dependent. J. Biol. Chem. 273:20860-20866.
Hortsch, M., Avossa, D., Meyer, D.I. 1986. Characterization of secretory protein translocation: ribosome-membrane interaction in endoplasmic reticulum. J. Cell Biol. 103:241-253.
Jackson, M.R., Nilsson, T., Peterson, P.A. 1993. Retrieval of transmembrane proteins to the endoplasmic reticulum. J. Cell Biol. 121:317-333.
Klumperman, J., Schweizer, A., Clausen, H., Tang, B.L., Hong, W., Oorschot, V., Hauri, H.-P. 1998. The recycling pathway of protein ERGIC-53 and dynamics of the ER-Golgi intermediate compartment. J. Cell Sci. 111:3411-3425.
Kuroda, R., Kinoshita, J., Honsho, M., Mitoma, J., Ito, A. 1996. In situ topology of cytochrome b(5) in the endoplasmic reticulum membrane. J. Biochem. (Tokyo). 120:828-833.
Kutay, U., Hartmann, E., Rapoport, T.A. 1993. A class of membrane proteins with C-terminal anchor. Trends Cell Biol. 3:72-75.
Kutay, U., Ahnert-Hilgen, G., Hartmann, E., Wiedenmann, B., Rapoport, T.A. 1995. Transport route for synaptobrevin via a novel pathway of insertion into the endoplasmic reticulum membrane. EMBO (Eur. Mol. Biol. Organ.) J. 14:224-231.
Letourneur, F., Cosson, P. 1998. Targeting to the endoplasmic reticulum in yeast cells by determinants present in transmembrane domains. J. Biol. Chem. 273:33273-33278.
Lippincott-Schwartz, J., Yuan, L.C., Bonifacino, J.S., Klausner, R.D. 1989. Rapid redistribution of Golgi proteins into the ER in cells treated with brefeldin A: evidence for membrane cycling from Golgi to ER. Cell. 56:801-813.
Lotti, L.V., Mottola, G., Torrisi, M.R., Bonatti, S. 1999. A different intracellular distribution of a single reporter protein is determined at steady state by KKXX or KDEL retrieval signals. J. Biol. Chem. 274:10413-10420.
Martire, G., Mottola, G., Pascale, M.C., Malagolini, N., Turrini, I., Serafini-Cessi, F., Jackson, M.R., Bonatti, S. 1996. Different fate of a single reporter protein containing KDEL or KKXX targeting signals stably expressed in mammalian cells. J. Biol. Chem. 271:3541-3547.
Masaki, R., Yamamoto, A., Tashiro, Y. 1996. Membrane topology and retention of microsomal aldehyde dehydrogenase in the endoplasmic reticulum. J. Biol. Chem. 271:16939-16944.
Nicchitta, C.V., Migliaccio, G., Blobel, G. 1991. Biochemical fractionation and assembly of the membrane components that mediate nascent chain targeting and translocation. Cell. 65:587-598.
Ozols, J. 1989. Structure of cytochrome b(5) and its topology in the microsomal membrane. Biochim. Biophys. Acta. 997:121-130.
Park, S.S., Walker, W., Aoyama, T., Lapenson, D.P., Waxman, D.J., Gonzales, F.J., Gelboin, H.V. 1992. Monoclonal antibodies to rat liver microsomal cytochrome b5. Biochem. Pharmacol. 43:2201-2208.
Pedrazzini, E., Villa, A., Borgese, N. 1996. A mutant cytochrome b5 with a lengthened membrane anchor escapes from the endoplasmic reticulum and reaches the plasma membrane. Proc. Natl. Acad. Sci. USA. 93:4207-4212.
Pelham, H.R.B., Munro, S. 1993. Sorting of membrane proteins in the secretory pathway. Cell. 75:603-605.
Pryde, J.G., Farmaki, T., Lucocq, J.M. 1998. Okadaic acid induces selective arrest of protein transport in the rough endoplasmic reticulum and prevents export into COPII-coated structures. Mol. Cell. Biol. 18:1125-1135.
Rayner, J.C., Pelham, H.R.B. 1997. Transmembrane domain-dependent sorting of proteins to the ER and plasma membrane in yeast. EMBO (Eur. Mol. Biol. Organ.) J. 16:1832-1841.
Roth, J., Wang, Y., Eckhardt, A.E., Hill, R.L. 1994. Subcellular localization of the UDP-N-acetyl-D-galactosamine: polypeptide N-acetylgalactosaminyltransferase-mediated O-glycosylation reaction in the submaxillary gland. Proc. Natl. Acad. Sci. USA. 91:8935-8939.
R?ttger, S., White, J., Wandall, H.H., Olivo, J.-C., Stark, A., Bennett, E.P., Whitehouse, C., Berger, E.G., Clausen, H., Nilsson, T. 1998. Localization of three human polypeptide GalNAc-transferases in HeLa cells suggests initiation of O-linked glycosylation throughout the Golgi apparatus. J. Cell Sci. 111:45-60.
Sato, K., Sato, M., Nakano, A. 1997. Rer1p as common machinery for the endoplasmic reticulum localization of membrane proteins. Proc. Natl. Acad. Sci. USA. 94:9693-9698.
Sato, M., Sato, K., Nakano, A. 1996. Endoplasmic reticulum localization of Sec12p is achieved by two mechanisms: Rer1p-dependent retrieval that requires the transmembrane domain and Rer1p-independent retention that involves the cytoplasmic domain. J. Cell Biol. 134:279-293.
Schweizer, A., Fransen, J.A.M., Bachi, T., Ginsel, L., Hauri, H.-P. 1988. Identification, by a monoclonal antibody, of a 53-kD protein associated with a tubulo-vesicular compartment at the cis-side of the Golgi apparatus. J. Cell Biol. 107:1643-1653.
Schweizer, A., Clausen, H., van Meer, G., Hauri, H.-P. 1994. Localization of O-glycan initiation, sphingomyelin synthesis, and glycosylceramide synthesis in Vero cells with respect to the endoplasmic reticulum-Golgi intermediate compartment. J. Biol. Chem. 269:4035-4041.
Seelig, H.P., Schranz, P., Schr?ter, H., Wiemann, C., Renz, M. 1994. Macrogolgin—a new 376 kD Golgi complex outer membrane protein as target of antibodies in patients with rheumatic disease and HIV infections. J. Autoimmun. 7:67-91.
Sonnichsen, B., Fullekrug, J., Nguyen Van, P., Diekmann, W., Robinson, D.G., Mieskes, G. 1994. Retention and retrieval: both mechanisms cooperate to maintain calreticulin in the endoplasmic reticulum. J. Cell Sci. 107:2705-2717.
Springer, S., Spang, A., Schekman, R. 1999. A primer on vesicle budding. Cell. 97:145-148.
Storrie, B., White, J., Rottger, S., Stelzer, E.H.K., Sugunuma, T., Nilsson, T. 1998. Recycling of Golgi-resident glycosyltransferases through the ER reveals a novel pathway and provides an explanation for nocodazole-induced Golgi scattering. J. Cell Biol. 143:1505-1521.
Subramaniam, V.N., Krijnse-Locker, J., Tang, B.L., Ericsson, M., Yusoff, A.R., Griffiths, G., Hong, W. 1995. Monoclonal antibody HFD9 identifies a novel 28 kD integral membrane protein on the cis-Golgi. J. Cell Sci. 108:2405-2414.
Teasdale, R.D., Jackson, M.R. 1996. Signal-mediated sorting of membrane proteins between the endoplasmic reticulum and the Golgi apparatus. Annu. Rev. Cell Dev. Biol. 12:27-54.
Tomita, M., Marchesi, V.T. 1975. Amino-acid sequence and oligosaccharide attachment sites of human erythrocyte glycophorin. Proc. Natl. Acad. Sci. USA. 72:2964-2968.
Velasco, A., Hendricks, L., Moremen, K.W., Tulsiani, D.R., Touster, O., Farquhar, M.G. 1993. Cell type-dependent variations in the subcellular distribution of alpha-mannosidase I and II. J. Cell Biol. 122:39-51.
Vergères, G., Yen, T.S., Aggeler, J., Lausier, J., Waskell, L. 1993. A model system for studying membrane biogenesis. Overexpression of cytochrome b5 in yeast results in marked proliferation of the intracellular membrane. J. Cell Sci. 106:249-259.
Vergères, G., Ramsden, J., Waskell, L. 1995. The carboxyl terminus of the membrane-binding domain of cytochrome b5 spans the bilayer of the endoplasmic reticulum. J. Biol. Chem. 270:3414-3422.
Yang, M., Ellenberg, J., Bonifacino, J.S., Weissman, A.M. 1997. The transmembrane domain of a carboxyl-terminal anchored protein determines localization to the endoplasmic reticulum. J. Biol. Chem. 272:1970-1975.
Yoshida, A., Suzuki, M., Ikenaga, H., Takeuchi, M. 1997. Discovery of the shortest sequence motif for high level mucin-type O-glycosylation. J. Biol. Chem. 272:16884-16888.
Yu, Y., Zhang, Y., Sabatini, D.D., Kreibich, G. 1989. Reconstitution of translocation-competent membrane vesicles from detergent-solubilized dog pancreas rough microsomes. Proc. Natl. Acad. Sci. USA. 86:9931-9935.
Yu, Y., Sabatini, D.D., Kreibich, G. 1990. Antiribophorin antibodies inhibit the targeting to the ER membrane of ribosomes containing nascent secretory polypeptides. J. Cell Biol. 111:1335-1342.(Emanuela Pedrazzinia, Antonello Villaa,b)